頁籤選單縮合
題 名 | Mild Hypokalemia Unveils the Footprint of Light-Chain Proximal Tubulopathy with Crystalline Formation |
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作 者 | Ling, Eng-kian; Tsai, Ming-hsien; Lin, Bing-shi; Yang, An-hang; Hsieh, Shih-chung; | 書刊名 | 臺灣腎臟醫學會雜誌 |
卷 期 | 26:4 2012.12[民101.12] |
頁 次 | 頁239-242 |
分類號 | 415.597 |
關鍵詞 | Multiple myeloma; Light chain tubulopathy; Hypokalemia; Fanconi syndrome; |
語 文 | 英文(English) |
英文摘要 | Hypokalemia is a common clinical problem and can be caused by several reasons, including renal potassium wasting, gastrointestinal loss, poor food intake and intercellular shifting of potassium ions. More often, we pay less attention to hypokalemia, particularly when it is not severe or when it can be corrected quickly by potassium replacement via the oral or intravenous route. However, the actual cause underlying the development of hypokalemia is not often determined and this occasionally results in treatment delay. Herein, we reported a rare case of multiple myeloma (MM) with κ light-chain proximal tubulopathy with crystalline formation. Our patient presented with mild and persistent hypokalemia for 6 months without further evaluation until MM-related Fanconi syndrome was finally diagnosed. Generally, the clinical clues leading to suspicion of MM are ypercalcemia, acute renal failure, bone lesions, unknown anemia, or reversed albumin-globulin ratio. Mild hypokalemia due to Fanconi syndrome as the primary presentation of MM is rare and may easily be neglected. Therefore, on the basis of this case, we want to stress the importance of determining the exact cause of any hypokalemia, because unexpected results may be found incidentally. |
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