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相關文獻
- Jeiunojejunal Intussusception due to Peutz-Jeghers Syndrome: Report of a Case and Review of the Literature
- Intussusception Caused by Peutz-Jeghers Syndrome: A Case Report and Literature Review
- Adult Duodenal-duodenal Intussusceptions with Hamartoma: A Rare Case Report
- Brunner's Gland Hamartoma of the Duodenum Presenting with Intussusception: Report of a Case
- Mesenchymal Hamartoma of the Liver: A Case Report
- 後天性平滑肌缺陷瘤
- 漫談小兒腸套疊
- Adult Intussusception Induced by Colonic Lipoma: A Case Report
- Sigmoid Colon Intussusception--Presenting as Rectal Prolapse
- 成人腸套疊之臨床經驗與分析
頁籤選單縮合
題 名 | Intussusception Caused by Peutz-Jeghers Syndrome: A Case Report and Literature Review=Peutz-Jeghers症候群引起腸套疊個案報告 |
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作 者 | 許志宏; 楊雅惠; 蔡志宏; 吳鴻昇; 洪敏章; 巫奕儒; 周德敖; 楊志宗; 黃明和; | 書刊名 | 秀傳醫學雜誌 |
卷 期 | 7:3 2007.10[民96.10] |
頁 次 | 頁111-114 |
分類號 | 415.47 |
關鍵詞 | 腸套疊; 缺陷瘤; Peutz-Jeghers syndrome; Intussuception; Harmatomas; |
語 文 | 英文(English) |
中文摘要 | Peutz-Jeghers syndrome (PJS) 雖然己經有很多報告描述過,但仍然是一種罕見的遺傳性瘜肉症候群合併有粘膜與皮膚的染色,特別常見於二十歲左右的患者,常常因為腸瘜肉造成併發症。 我們報告一小腸阻塞病例,患者有間歇性腹部抽痛及大量的嘔吐。腹部超音波檢查發現上部腹部有一個大的標靶徵象,腹部電腦斷層透露了空腸套疊。患者因此接受了開腹、腸套疊復位及空腸部份切除手術。病理組織報告顯示有許多缺陷瘤,最大一個大小為直徑四公分。患者的手術復原良好。我們報告這罕見的案例並回顧文學,且建議對於這種病例應該長期追蹤以便及早發現癌變的可能。 |
英文摘要 | Peutz-Jeghers syndrome (PJS) is a rare, though well-described, hereditary polyposis syndrome associated with mucocutaneous pigmentation that typically presents in the second decade of life with complications related to intestinal polyps. We report a case of intestinal obstruction associated with intermittent abdominal cramping pain and copious vomiting. Ultrasonography revealed a large target sign lesion over the upper abdomen. Computerized tomography of the abdomen disclosed jejunal intussuception. Exploratory surgery with reduction and segmental resection of the involved jejunum was performed. Histopathologic study revealed numerous hamartomas, with the biggest one measuring 4cm in diameter. The patient's post-operative course was uneventful. Herein, we report on this rare case, review the literature, and suggest long-term follow up of these kind of cases to early detect malignancy. |
本系統中英文摘要資訊取自各篇刊載內容。