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題 名 | Keratoderma Plantaris and Mechanic's Hands as the Initial Presentation in a Case of Dermatomyositis=一個以蹠部角皮症和機械手為初始表現的皮肌炎 |
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作 者 | 張力元; 楊麗珍; 吳詹永嬌; | 書刊名 | 中華皮膚科醫學雜誌 |
卷 期 | 20:4 2002.12[民91.12] |
頁 次 | 頁329-334 |
分類號 | 415.762 |
關鍵詞 | 皮肌炎; Dermatomyositis; Mechanic's hands; Acquired palmoplantar keratoderma; |
語 文 | 英文(English) |
中文摘要 | 六十四歲女性一開始是以手指腹面和側面以及腳趾會癢且裂隙角質增生的斑塊擴展到兩手掌和腳掌來表現,體重也減輕四公斤。臆測診斷為後天掌蹠角化症。檢查後沒有惡性的發現,每天服用Acitretin 25毫克治療後,症狀大輻改善。不幸的是,三個月後出現近端肌肉無力。後來在兩膝蓋和指間關節的背面出現會癢、紅到暗紅色的丘疹及斑塊,上背部出現血管性萎縮性皮膚異色樣外觀。血清肌氨酸甘磷激素上升。診斷為皮肌炎而且以機械手為起始表現。在給予高劑量類固醇治療後,肌肉強度恢復而且機械手也改善。機械手可以是結締組織疾病伴隨疾病發炎性肌炎的標誌和初始表現。 |
英文摘要 | A 64-year-old woman initially presented with itching and fissuring hyperkeratotic plaques on the ventral and lateral sides of fingers and toes with extension to both palms and soles. A Body weight loss of 4 kg was also complained. Tentative diagnosis of acquired palmoplantar keratoderma was made. The patient responded quite well to Acitretin 25 mg daily. She underwent a malignancy survery, which was negative. Unfortunately, progressive proximal muscle weakness occurred three months later. Itching erythematous to ducky red papules or plaques on bilateral knees and dorsal aspects of the interphalangeal joints and poikilodermatous appearance on the upper back were found thereafter. An increased level of serum creatinine phosphokinase (CPK) was demonstrated. Dermatomyositis with mechanic’s hands as the initial manifestation was diagnosed. Muscle strength regained and mechanic’s hands improved when high doses of corticosteroids were administered. Mechanic’s hands may be a marker and first presentation for connective tissue diseases associated with inflammatory myositis. |
本系統中英文摘要資訊取自各篇刊載內容。