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題 名 | Hypereosinophilic Syndrome--A Case Report=嗜伊紅白血球增多症--一病例報告 |
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作 者 | 藍斐君; 洪大川; 周友三; 蔡正河; | 書刊名 | Acta Cardiologica Sinica |
卷 期 | 14:4 民87.10-12 |
頁 次 | 頁213-219 |
分類號 | 415.615 |
關鍵詞 | 嗜伊紅白血球增生; 心內膜; 心臟超音波; Hypereosinophilia; Endocardium; Echocardiography; |
語 文 | 英文(English) |
中文摘要 | 背景:嗜伊紅白血球增多症為一長期,原因不明之嗜伊紅白血球增生現象,常伴 隨心臟以及其他一種或多種器官之侵犯。 病例報告:本文報告一位 32 歲成年女性因原因不明之發燒及嗜伊紅白血球增多症入院治療 。在臨床症狀出現後大約一個月病例報告,心臟超音波即有心內膜纖維化之增厚及左心室腔 血栓填塞。 僅經過三天之化學治療,嗜伊紅白血球之增多,胸部 X 光及臨床症狀即呈現明 顯改善。雖然嗜伊紅白血球之數目已控制在 1200/mm �纂A數天後病人仍因感染革蘭氏陰性 桿菌敗血症而死亡。 結論:心臟為嗜伊紅白血球增多症病變器官之一。心臟病變亦可出現在早期的病程中。心臟 超音波乃是一種診斷及監測心臟病變的便利工具。仔細投與藥物或外科治療應可幫助各個不 同病程的症狀。積極的化學治療來控制嗜伊紅白血球的數目似乎對此類病患有著正面的影響 。 |
英文摘要 | Background. Hypereosinophilic syndrome (HES) is defined as an unexplained and prolonged overproduction of eosinophils that leads to infiltration and damage of one or more organs, including the heart. Clinical, echocardiographic, and roentgenographic characteristics in an adult female with HES are reported. Unlike previous reports of echocardiography in HES, in this case, endomyocardial change was already present one month after the disease had developed. Methods and Results. A 32 year-old female suffered from an unexplained fever with increase of eosinophils, florid manifestations of skin, and cardiac, respiratory, gastrointestinal, hepatic, splenic and bone marrow involvement. Endomyocardial fibrotic thickening and thrombus obliterating the apex of the left ventricle (LV) were documented by transthoracic and transesophageal echocardiography one month after eosinophilia was detected. Clinical improvement was evident within 3 days after beginning treatment directed at controlling the eosinophilia. Nevertheless, the patient died 3 days after her eosinophil count had dropped to less than 1200/mm��. Conclusions. Heart disease should be suspected in any patient with sustained eosinophilia, whether the eosinophilia is thought to be benign or malignant. Early heart damage in HES is possible. Two-dimensional echocardiography is a useful tool to diagnose or follow such cardiac changes. Careful medical and/or surgical management of heart dysfunction should be offered to patients, depending on the stage of the disease. Aggressive chemotherapy to suppress eosinophils to normal number seems to have positive influence on the outcome of HES. |
本系統中英文摘要資訊取自各篇刊載內容。