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題 名 | Diffuse Type Pulmonary Arteriovenous Malformations: Report of One Case=廣泛性肺動靜脈畸形:一病例報告 |
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作 者 | 游昌憲; 陳銘仁; 林炫沛; 施並富; | 書刊名 | 臺灣兒科醫學會雜誌 |
卷 期 | 46:1 民94.01-02 |
頁 次 | 頁27-30+53 |
分類號 | 415.38 |
關鍵詞 | 廣泛性肺動靜脈畸形; 對比心臟超音波; 鎝標定血清蛋白巨凝物之肺灌注掃描; Diffuse pulmonary arteriovenous malformations; Contrast echocardiography; Technetium-labeled macroaggregated albumin; |
語 文 | 英文(English) |
英文摘要 | Pulmonary arteriovenous malformations are direct communications between pulmonary arteries and veins via a tortuous vascular space. They can cause severe pulmonary and neurologic complications. Most PAVMs are located in the lower lobes and can be seen on radiography or angiography. However, a few patients with PAVMs have a more severe and diffuse pattern of disease. These patients generally present with more profound cyanosis and a poorer prognosis. The widespread distribution and small size of these lesions make both diagnosis and management very difficult. We report a 12-year-old patient with diffuse bilateral PAVMs confirmed by contrast echocardiography and technetium-labeled macroaggregated albumin perfusion scan. |
本系統中英文摘要資訊取自各篇刊載內容。