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題名 | 顏面部隆突性皮膚纖維肉瘤--病例報告=Dermatofibrosarcoma Protuberans of the Face--Case Report and Literature Review |
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作者 | 王奕凱; 楊安航; 雷文天; 吳政憲; 高壽延; Wang, I-kai; Yan, An-han; Lui, Men-tin; Wu, Cheng-hsien; Kao, Shou-yen; |
期刊 | 中華民國口腔顎面外科學會雜誌 |
出版日期 | 20060900 |
卷期 | 17:2 民95.09 |
頁次 | 頁117-127 |
分類號 | 416.954 |
語文 | chi |
關鍵詞 | 隆突性皮膚纖維肉瘤; 顏面部; Dermatofibrosarcoma protuberans; DFSP; Face; |
中文摘要 | 隆突性皮膚纖維肉瘤(dermatofibrosarcoma protuberans, DFSP)是一種罕見的低度惡性皮膚腫瘤,它的生長速度雖很慢但具有局部侵襲性及容易復發等特性。此種腫瘤好發於軀幹及近端四肢,在頭頸部區域較為少見,所佔比例約12%到15%。在組織學上,腫瘤主要由梭狀細胞嵌於膠原纖維基質,並且排列成特殊的旋渦狀,扇狀或輪狀結構。早期的DFSP常被病人忽視且被醫師視為良性病灶,而保守性的外科手術切除導致相當高比率的局部復發。本篇文章將提出一例臺北榮總口腔顎面外科患者其顏面部隆突性皮膚纖維肉瘤之病例報告,對其臨床及病理上的表現、診斷、治療作一敘述並回顧相關文獻。 |
英文摘要 | Dermatofibrosarcoma protuberans (DFSP) is a rare, slow-growing, locally invasive, low grade mesenchymal malignant neoplasm that originates from the dermis. It usually present as nodular cutaneous mass on the trunk and proximal extremities. Only 12% to 15% of the cases are localized in the head and neck region. Microscopically, it consists of uniform but atypical spindle cells in a fibrous stroma, forming a characteristic storiform pattern. DFSP is often dismissed by patients and misdiagnosed by physicians as benign lesion in the early stage. Conservative surgical management results in a high local recurrence rate. This paper presents a case of DFSP of the face which was diagnosed and treated at the oral and maxillofacial surgery department of Taipei Veterans General Hospital. A literature review is conducted to highlight the clinicopathological presentation and management of this rare tumor. |
本系統之摘要資訊系依該期刊論文摘要之資訊為主。