查詢結果分析
來源資料
頁籤選單縮合
題名 | Wiskott-Aldrich氏症候群患者之牙科考量--病例報告=Dental Considerations for the Patient with Wiskott-Aldrich Syndrome: Report of a Case |
---|---|
作者 | 陳明宏; 張川陽; 蔡佩芬; 邱宏仁; 張哲豪; 石佳弘; 許修銘; | 書刊名 | 臺灣兒童牙醫學雜誌 |
卷期 | 6:1 民95.03 |
頁次 | 頁214-219 |
分類號 | 417.69 |
關鍵詞 | Wiskott-Aldrich氏症候群; 造血細胞移植; 牙科考量; Wiskott-aldrich syndrome; Hematopoietic cell transplantation; Dental considerations; |
語文 | 中文(Chinese) |
中文摘要 | Wiskott-Aldrich氏症候群是一種X染色體隱性的性聯遺傳的罕見疾病,患者最主要的3個臨床症狀為血小板數量低下、濕疹、和免疫力缺乏。患者多為女性,通常在2~3個月大時便出現症狀。大多數患者在兒童時期便會死亡,除非骨髓移植成功才能有較高的存活率。本病例報告將討論一位罹患Wiskott-Aldrich氏症候群之11歲男孩,即將於小兒科接受造血細胞移植。我們將就Wiskott-Aldrich氏症候群之臨床症狀、牙科照護之血液值方面考量、及造血細胞移植前之牙科考量,做一文獻回顧及討論。 |
英文摘要 | Wiskott-Aldrich syndrome is a rare, x-linked recessive hereditary disease, mostly affecting male patients. The common expressions of this disease include a triad: thrombocytopenia, eczema, and immunodeficiency. Those who are affected often have symptoms by the age of 2-3 months old, and mostly die in their childhood unless bone marrow transplantation was successfully performed. This case report reviewed the literatures and described an 11-year-old male patient with Wiskott-Aldrich, who is going to receive hematopoietic cell transplantation. We discussed the clinical symptoms and sings of Wiskott-Aldrich syndrome, hematological considerations for dental care, and dental procedures before hematopoietic cell transplantation. |
本系統之摘要資訊系依該期刊論文摘要之資訊為主。