查詢結果分析
相關文獻
- Coexistence of Lymphangioleiomyomatosis and Angiomyolipomas in a Patient of Tuberous Sclerosis Complex: A Case Report
- Renal Angiomyolipoma: A Case Report
- Tuberous Sclerosis with Visceral Organ Involvement
- Clinicopathologic Analysis of Renal and Extrarenal Angiomyolipomas: Report of 44 Cases
- Growth Pattern of Renal Angiomyolipoma on Computed Tomography: Report of Two Cases
- Angiomyolipoma of the Liver: Case Report
- High-Resolution Computed Tomography in Pulmonary Lymphangio(leio)myomatosis and Pulmonary Tuberous Sclerosis
- The Management Strategy of Renal Angiomyolipoma
- Renal Angiomyolipoma with Lymph Node Involvement: A Case Report and Literature Review
- Angiomyolipoma of the Liver: A Case Report
頁籤選單縮合
題 名 | Coexistence of Lymphangioleiomyomatosis and Angiomyolipomas in a Patient of Tuberous Sclerosis Complex: A Case Report=同時出現lymphangioleiomyomatosis及血管肌肉脂肪瘤的結節硬化症病例:病例報告 |
---|---|
作 者 | 謝豐吉; 劉高郎; 張逸良; 李文正; 曾旭明; | 書刊名 | 中華放射線醫學雜誌 |
卷 期 | 28:5 2003.10[民92.10] |
頁 次 | 頁329-333 |
分類號 | 416.224 |
關鍵詞 | 淋巴平滑肌瘤症; 血管肌肉脂肪瘤; 結節硬化症; Angiomyolipoma; Lymphangioleiomyomatosis; Tuberous sclerosis complex; |
語 文 | 英文(English) |
中文摘要 | 肺部lymphangioleiomyomatosis(LAM)是一種罕見的疾病。它的臨床症狀、放射學特徵以及病理組織上都與結節硬化症的肺部表徵一致。LAM同時伴隨兩側、多發的血管肌肉脂肪瘤並非不常見。有些學者猜測LAM是結節硬化症的一種。我們報告一個案,一開始認為是LAM。在做肺臟移植前的評估時,意外發現兩側腎臟有多發的血管肌肉脂肪瘤。此病人同時符合結節硬化症的診斷標準。我們並且討論LAM及結節硬化症的關係。 |
英文摘要 | Pulmonary lymphangioleiomyomatosis (LAM) is a rare disease. The symptoms, radiological features and histopathological evidences are identical to that of pulmonary involvement of tuberous sclerosis complex (TSC). Coexistence of renal angiomy-olipomas (AMLs), especially multiple and bilateral sides is often observed. Some investigators have pro-posed that LAM may be a forme fruste of TSC. We present a case that was firstly diagnosed as LAM and then bilateral multiple renal AMLs were found during pre-transplant evaluation. The case also met the diagnostic criteria of TSC. We discuss the rela-tionship between LAM and TSC. |
本系統中英文摘要資訊取自各篇刊載內容。