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來源資料
頁籤選單縮合
題 名 | Intraductal Papillary Neoplasm of the Pancreas=胰臟管內乳突腺腫瘤 |
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作 者 | 黃天立; 石宜銘; 蘇正熙; 羅世薰; 蔡世豪; 吳秋文; 雷永耀; | 書刊名 | 中華民國外科醫學會雜誌 |
卷 期 | 29:4 民85.07-08 |
頁 次 | 頁311-315 |
分類號 | 416.248 |
關鍵詞 | 胰臟管; 乳突腺腫瘤; Intraductal papillary neoplasm; Mucinous cystic neoplasm; Pylorus-preserving pancreaticoduodenectomy; |
語 文 | 英文(English) |
中文摘要 | 從1982年Ohhashi首篇報告以來,關於胰臟管內乳突腺腫瘤的文獻相繼提 出討論。目前,在命名和臨床病理上仍存有相當的爭議性。從1985年至1994年, 本院共有4例胰臟管內乳突腺瘤,從病人年齡、性別、腫瘤的大小、位置、臨床 表徵、和病理上分別加以討論。我們的結論是胰臟管內乳突腺瘤是特一的臨床疾 病。由於,它具惡性傾向,治療上以積極外科手術切除為主。 |
英文摘要 | Controversies about both the term for and clinicopathologic entity of theintraductal papillary neoplasm of the pancreas still exist. The incidence ofthis tumor is rare, with only a few cases reported in the literature. Fourcases of intraductal papillary adenocarcinoma of the pancreas, treated atthe Veterans General Hospital-Taipei, between January 1985 and December1994 were re-viewed retrospectively. The age, sex, size, tumor location, clinical presentation, pathology and prognosis were re-evaluated for each patient. All patients were male, aged from 63 to 79 years. Tumor sizes variedfrom 2.5 to 6 cm, and all were located in the head of the pancreas. The mostcommon presentations were weight loss, epigastric pain, and jaundice.Grossly, these appeared as papillary soft tumors occluding the main pancreatic duct, with well-differentiated, mucin-secreting, columnar epithelialcells along the dilated pancreatic ducts. Three patients, who had receivedpylorus-preserving pancreaticoduodenectomy (PPPD), survived with amean follow-up of 22.7 months (range: 18-30 months). The other patient wasunresectable, but received a bypass operation with a survival of 19.5months. The intraductal papillary neoplasm is a unique clinicopathologicalentity compared with mucinous cystic neoplasm and classic duct adenocarcinoma of the pancreas. Clinically, the typical endoscopic retrograde cholangiopan-creaticographic (ERCP) findings, plus a cystic mass in the pancreatic head found by ultrasound or CT scans should lead to the diagnosisof intraductal papillary neoplasm of the pancreas. Aggressive surgical procedure should be attempted for this mucin-producing neoplasm with low-grade malignancy. |
本系統中英文摘要資訊取自各篇刊載內容。