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頁籤選單縮合
題 名 | CT and Surface Shaded Model of Madelung's Disease: A Case Report=梅德倫疾病之電腦斷層及表面重組表徵:病例報告 |
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作 者 | 江國賢; 嚴寶勝; 許永祥; 李超群; 張寶源; 周紹賓; | 書刊名 | 中華放射線醫學雜誌 |
卷 期 | 29:3 2004.06[民93.06] |
頁 次 | 頁143-146 |
分類號 | 415.96 |
關鍵詞 | 電腦斷層; 表面重組; 梅德倫疾病; Computed tomography; CT; Image processing; Madelung's disease; |
語 文 | 英文(English) |
中文摘要 | 梅德倫疾病是一種罕見的疾病,在東方人中更少見。患者多有酒癮,其病理機制尚未明確,可能與粒腺體的基因缺陷有關。我們報告一名四十六歲男性病患,因多年頸部及下頜腫大來求診,電腦斷層顯現患部呈現均勻脂肪組織浸潤,並未侵犯深層器官。經表面重組後可見兩頰、下頜及頸部對稱性腫大,為典型梅德倫疾病症狀。除了傳統電腦斷層掃描外,表面重組亦可提供三度空間的術前評估。 |
英文摘要 | Madelung’s disease is rare in the Chinese community. It usually happens in patients with alcoholism. The etiology is unknown and probably relates to mitochondrial disease. We report a 46-year-old male who complaint of submental and neck swelling for many years. Computed tomography (CT) shows prominent fat at the anterior neck region extended from bilateral buccal area to the suprasternal notch, and posteriorly at the occipital to upper back region. Surface shaded model demonstrats grotesque symmetrical enlargement of the soft tissue around buccal to anterior neck region with typical “horse collar” and “hamster cheek” appearance which is diagnostic for Madelung’s disease. Preoperative CT and surface shaded model play a major role in the treatment planning of Madelung’s disease. |
本系統中英文摘要資訊取自各篇刊載內容。