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題 名 | High-Resolution Computed Tomography of Pulmonary Alveolar Microlithiasis=肺泡微石症之高解析胸部電腦斷層檢查所見:一病例報告 |
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作 者 | 張允中; 楊泮池; 陸坤泰; 曾旭明; 蘇誠道; | 書刊名 | 臺灣醫學會雜誌 |
卷 期 | 98:6 1999.06[民88.06] |
頁 次 | 頁440-443 |
分類號 | 415.46 |
關鍵詞 | 肺泡微石症; 高解析胸部電腦斷層檢查; Alveolar microlithiasis; Calcinosis; Computed tomography; |
語 文 | 英文(English) |
英文摘要 | Pulmonary alveolar microlithiasis (PAM) is a rare disease. It has been reported predominantly in Turkey. We report a case of PAM with characteristic high-resolution computed tomography (CT) findings. A 45-year-old Taiwanese woman had progressive difficulty in breathing for 7 years. Her chest radiographs showed diffuse high-density micronodules and reticular lines that obliterated the bronchovascular bundles and the margin of the heart and diaphragm. The micronodules were scattered throughout both lung fields with basal predominance. Examination of a transbronchial lung biopsy specimen showed PAM. High-resolution CT showed a unique and characteristic calcified reticular pattern and thickening of the interlobular septa of the lung parenchyma, with predominant basal and peripheral lung distribution. Reticulonodular changes of the interlobular septa and intralobular interstitial lines associated with subpleural air cysts and paraseptal emphysema were evident. These high-resolution CT findings are pathognomonic for PAM. Thus, lung biopsy may be avoided in the presence of this characteristic finding. |
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