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相關文獻
- Use of Laryngeal Mask Airway for the Resuscitation of a Hunter Syndrome Patient during General Anesthesia Induction
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題 名 | Use of Laryngeal Mask Airway for the Resuscitation of a Hunter Syndrome Patient during General Anesthesia Induction=喉頭罩呼吸道在全身麻醉誘導時成功地使用於杭特徵候群之急救 |
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作 者 | 陳志豪; 黃國巡; 李長光; 黃元修; 汪志雄; | 書刊名 | Journal of Medical Sciences |
卷 期 | 23:6 2003.12[民92.12] |
頁 次 | 頁351-354 |
分類號 | 416.5 |
關鍵詞 | 喉頭罩呼吸道; 杭特徵候群; Hunter syndrome; Laryngeal mask airway; Mucopolysaccharidoses; |
語 文 | 英文(English) |
英文摘要 | Hunter syndrome (mucopolysaccharidoses, type II; MPS II) is made up of a rare group of inherited recessive connective tissue diseases. The most important implications of this syndrome to anesthesiologists are airway management and tracheal intubation. We presented a patient with Hunter syndrome who received emergent exploratory laparotomy with enterolysis and multiple drainage due to massive ascites with comprised ventilation. Intubation general anesthesia was planned for this patient, but tracheal intubation failed. Mask ventilation was also difficult due to bizarre airway anatomy. Bradycardia and subsequent asystole developed in this patient. Laryngeal mask airway (LMA) was inserted and acceptable ventilation was established. We resuscitated him and tracheostomy was performed. The patient was sent to the pediatric intensive care unit for further care and was transferred to the general ward without any sequeala 2 days after surgery. In this case, the LMA has been used successfully in emergent difficult intubations and we believe that tracheostomy is necessary for the long-term airway management of the MPS patients. |
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