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題 名 | Dentinogeneis Imperfecta Associated with Osteogenesis Imperfecta: Report of Two Cases=牙本質發生不全合併成骨不全--二例報告 |
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作 者 | 蔡佳玲; 林瑩澤; 林雅婷; | 書刊名 | 長庚醫學 |
卷 期 | 26:2 2003.02[民92.02] |
頁 次 | 頁138-143 |
分類號 | 416.942 |
關鍵詞 | 牙本質發生不全; 成骨不全; 奶瓶性齲齒; Dentinogenesis imperfecta; Osteogenesis imperfecta; Nursing bottle caries; |
語 文 | 英文(English) |
中文摘要 | 成骨不全是遺傳性中胚葉的缺陷,而牙本質發生不全是牙器(odontogenic apparatus)的中胚層部分發生障礙,兩者可能聯點出。牙本質發生不全的牙齒外觀呈現特殊的透明性及乳光色澤,顏色從灰白色到黃褐色都有,比正常牙齒更容易磨損,但這類牙齒對齲的感受性並不比正常者大,反而較低。我們報告兩個年紀在早期混合齒列期的牙本質發生不全聯合成骨不全病例,其中一位患有奶瓶性齲齒。報告目的在於提出中等到輕微程度的成骨不全同時患有牙本質發生不全患者的口腔及顱骨特徵,並討論可能的牙科治療。成骨不全患者在乳牙剛萌出時即應由牙醫師做評估是否同時患有牙本全發生不全,牙科即時的介入衛教及處理將有助於減少廣泛而的牙科治療。 |
英文摘要 | Osteogenesis imperfecta (OI) is a heritable systemic disorder of the connective tissue. Dentinogenesis imperfecta (DI), which is sometimes an accompanying symptom of OI, belongs to a group of genetically conditioned dentin dysplasias and is characterized clinically by an opalescent amber appearance of the dentin. Although the teeth of DI cases wear more easily and excessively compared to normal teeth, they do not appear to be more susceptible to dental caries than normal teeth. Two cases of DI associated with OI are presented in this paper, with 1 case suffering from nursing bottle caries. The purposes of this paper are to present the dental and skeletal characteristics of moderately and mildly involved DI associated with OI, and to discuss the possible methods of dental treatment. Patients with OI and involvement and oral hygiene instruction ca be of help in reducing the necessity of extensive dental care. |
本系統中英文摘要資訊取自各篇刊載內容。