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題 名 | Retinal Capillary Hemangiomas: Clinical Manifestations and Visual Prognosis=視網膜微血管瘤之臨床表現及其預後 |
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作 者 | 郭明澤; 郭錫恭; 郭明倫; 蔡明勳; 陳勇仁; 林淑妍; | 書刊名 | 長庚醫學 |
卷 期 | 25:10 2002.10[民91.10] |
頁 次 | 頁672-682 |
分類號 | 416.746 |
關鍵詞 | 視網膜微血管瘤; 滲出性視網膜剝離; Retinal capillary hemangioma; von Hippel-Lindau disease; VHL; Exudative retinal detachment; |
語 文 | 英文(English) |
中文摘要 | 背景:為了進一步描術視網膜微血管瘤病患之臨床特徵,視力之預後,治療的效果及其併發症。 方法:迴顧及分析於1987到2001年在高雄長庚醫院的視網膜微血管瘤之病患,共有12位病患(13隻眼睛),特別針對這些病患治療前後的視力,臨床表現及眼球之併發症加以探討。 結果:12位病人之中,有一位是雙眼視神經旁各有一個視網膜微血管瘤,另一位是單眼視神經旁有一個視網膜微血管瘤,其餘10位病患皆為單眼週邊視網膜的視網膜微血管瘤。大部皆的視網膜微血管瘤病患其微血管瘤是位於視網膜顳側且這12位病人皆為內生型。這12位病人皆不符合von Hippel-Lindau disease之診斷要件。大部皆早期診斷的周邊視網膜微血管瘤病患接受局部雷射治療皆能維持原有之視力,有2位病患併發滲出性視網膜剝離而必須接受玻璃體視網膜手術治療。視神經旁視網膜微血管瘤病患不論治療與否,預後變異性大。 結論:早期診斷及以雷射治療周邊視網膜微血管瘤通常有不錯的預後。如果不加以治療,則可能會併發滲出性視網膜剝離而必須接受玻璃體視網膜手術治療而有較差之預後。 |
英文摘要 | Backgorund: to describe the clinical features, visual outcomes, and therapeutic complications of patients with retinal capillary hemangiomas. Methods: A retrospective, non-comparative, observational case study of patients diagnosed with retinal capillary hemangiomas was conducted. Twelve patients (13 eyes) at Chang Gung Memorial Hospital of Kaohsiung from July 1987 to June 2001 were reviewed. Pre-and post-treatment visual acuity and ocular complications are described. Results: One patient had bilateral and another had unilateral juxtapapillary hemangiomas. All of the other 10 patients were diagnosed with peripheral retinal capillary hemanagioomas. More patients had retinal capillary hemangiomas located in the temporal peripheral retina and all had endophytic growth patens. No patients met the diagnostic criteria of von Hippel-Lindau disease. Visual acuity levels of peripheral retinal hemangiomas without oxidative retinal detachment often remained the same after focal laser treatment. Two patients received vitreoretinal surgery. Patients with juxtapapillary hemangiomas had variable visual outcomes and visual field defects during follow-up. Conclusion: Early diagnosis of capillary hemangiomas in the retinal periphery and treatment by focal laser produced good visual outcomes. If untreated, the tumors may eventually be complicated with educative retinal detachment and have a worse visual prognosis even with vitreoretinal surgery. |
本系統中英文摘要資訊取自各篇刊載內容。