頁籤選單縮合
題 名 | 先天性鼻梨狀口狹窄之手術治療--兩例報告=Surgical Intervention for Congenital Pyriform Aperture Stenosis--Report of Two Cases |
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作 者 | 陳昱君; 李國森; 楊政謙; 張克昌; | 書刊名 | 中華民國耳鼻喉科醫學雜誌 |
卷 期 | 34:3 民88.05-06 |
頁 次 | 頁262-265 |
分類號 | 417.6853 |
關鍵詞 | 先天性鼻梨狀口狹窄; 後鼻孔閉鎖; 單一上門牙; Congenital pyriform aperture stenosis; Choanal atresia; Solitary maxillary central incisor; |
語 文 | 中文(Chinese) |
中文摘要 | 先天性鼻梨狀口狹窄為一罕見的新生兒先天性鼻呼吸道阻塞,其臨床症狀與雙側 後鼻孔閉鎖相似,鼻部電腦斷層檢查為一重要診斷依據。有報告指出先天性鼻梨狀口狹窄與 單一上門牙、前腦空洞症、染色體缺損、及荷爾蒙異常有關。治療方式以保守性療法為優先, 若因狹窄造成的臨床症狀無法改善時,則需實施手術治療。本科提出兩例先天性鼻梨狀口狹 窄之手術治療。手術方式經唇下路徑,利用骨膜剝離子、骨刮器、手術顯微鏡及鑽石磨骨器 拓寬鼻道,術後以矽膠管做支撐7天即可拔除,門診追蹤至今情況良好。 |
英文摘要 | Congenital pyriform aperture stenosis (CNPAS) is a rare cause of nasal airway obstruction in neonates and infants. The presenting symptoms, which include cyanosis during feeding or sleep which is relieved by crying, are similar to the symptoms of bilateral choanal atresia. Computed tomography scan of the nose is used for diagnosis. Reports have suggested its correlation to a solitary maxillary central incisor, holoprosencephaly, and endocrine insufficiency. We encountered two patients with CNPAS who received surgical intervention to relieve the symptoms after the conservative therapy had failed. After a sublabial incision and under the microscope, diamond burrs and bone curettes were applied to augment the nasal bony inlet. A silicon tube was then inserted as a stent for one week. Both patients were discharged with no signs of respiratory difficulty. We suggested that surgical intervention should be considered if a patient is younger than 4 months old, when a Fr.5 catheter can not be inserted through the nostril, while there is cyclic apnea, or when the conservative treatment fails. |
本系統中英文摘要資訊取自各篇刊載內容。