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頁籤選單縮合
題 名 | 非胰島素瘤胰臟性低血糖症候群--一病例報告及文獻回顧=Noninsulinoma Pancreatogenous Hypoglycemic Syndrome--A Case Report and Review of Literature |
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作 者 | 李亭儀; 楊宏智; 王繁芬; 翁錦興; 李美芝; 林宏達; 鄧錦泉; | 書刊名 | 內科學誌 |
卷 期 | 13:3 2002.06[民91.06] |
頁 次 | 頁133-140 |
分類號 | 415.6688 |
關鍵詞 | 低血糖; 非胰島素瘤胰原性低血糖症候群; 選擇性動脈鈣輸注試驗; Hypoglycemia; Noninsulinoma pancreatogenous hypoglycemic syndrome; NIPHS; Selective arterial calcium infusion test; |
語 文 | 中文(Chinese) |
中文摘要 | 胰島母細胞增殖是指胰臟小島細胞瀰漫或擴散性的增生,造成嬰兒和小孩胰島素分泌過多引致低血糖最常見的原因,但在成人則較為少見,也被稱為非胰島素瘤胰原性低血糖症候群(Noninsulionma Pancreatogenous Hypoglycemic Syndrome;NIPHS)。本篇是報告一個NIPHS的個案。一位75歲男性因昏迷被送到急診室,檢查發現血糖過低(血漿葡萄糖為33mg/d1),此時血清C-peptide濃度和胰島素濃度偏高,補充葡萄糖後意識完全恢復。病患沒有糖尿病史,近年常有飯後冒冷汗和全身無力的症狀,住院前也否認吃過任何藥物。病人72小時禁食試驗結果正常;C-peptide抑制試驗發現靜脈注射胰島素後無法抑制C-peptide分泌;Glucagon刺激試驗發現給藥後5分鐘C-peptide和胰島素濃度上升過高。選擇性動脈鈣輸注試驗發現於脾動脈、上腸系胰和胃十二指腸動脈在注射鈣後,胰島素濃度上升。因高度懷疑是NIPHS或胰島素瘤接受手術治療,手術中觸診及超音波並沒有發現腫瘤,進行胰臟尾部切除術,病理診斷確認是胰島母細胞增殖。術後空腹血糖上升到140mg/dL,經飲食治療後,血糖控制良好,兩年半的追蹤沒有發生低血糖。但不幸病人於2001年因慢性阻塞性肺疾病(COPD)在別的醫院去世,死亡原因與低血糖或本疾病無關。 |
英文摘要 | Nesidioblastosis is a diffuse proliferative process of pancreatic islet cells characterized by hyperinsulinemic hypoglycemia. This is a rare cause of hypoglycemia in adults and is presently designated as noninsulinoma pancreatogenous hypoglycemia syndrome (NIPHS). Here, we report a case. A 75 years old male patient found unconscious was send to our emergency room where inappropriate elevation of C-peptide and insulin level were found during hypoglycemia and his conscious recovered after glucose infusion. He has no history of diabetes and denied taking any medicine. He suffered from cold sweating and weakness recently. Seventy two-hour prolonged fasting was inconclusive, but C-peptide suppression test showed non-suppression of C-peptide 60 min after insulin infusion. Glucagon test showed an enhanced increment in insulin and C-peptide level 5 min after glucagon injection. CT scan of abdomen showed no tumor growth in the pancreas or other organs. Selective arteriography with calcium infusion test showed 2-3 fold increased in insulin level after calcium infusion at the splenic , superior mesenteric and gastroduodenal arteries. Explore laparotomy revealed no tumor in the pancreas and distal pancreactectomy was performed. Diagnosis of NIPHS was confirmed by pathological examination. No hypoglycemic episode was noted during this 2.5 years follow-up. Unfortunatel , he died of COPD unrelated to hypoglycemia or NIPHS at other hospital in 2001. |
本系統中英文摘要資訊取自各篇刊載內容。