查詢結果分析
來源資料
相關文獻
- Multiple Myeloma with Myelomatous Pleural Effusion--A Case Report
- 鼻腔髓外漿細胞瘤--病例報告
- Multiple Myeloma Presenting with a Paraspinal Tumor and Malignant Effusion: Case Report
- Immunoglobulin D Multiple Myeloma: A Case Report
- 多發性骨髓瘤--病例報告
- 當前多發性骨髓瘤治療與護理趨勢之探討
- Immunoglobulin D Multiple Myeloma
- Multiple Myeloma Associated with Extramedullary Plasmacytoma Causing Nerve Root Compression:A Case Report
- Intraoperative Stroke under Epidural Anesthesia for Bipolar Hemiarthroplasty in a Patient with Multiple Myeloma:A Case Report
- 多發性骨髓瘤與Thalidomide
頁籤選單縮合
題 名 | Multiple Myeloma with Myelomatous Pleural Effusion--A Case Report=多發性骨髓瘤合併骨髓瘤性肋膜積液--一病例報告 |
---|---|
作 者 | 洪啟超; 王鴻昌; 陳家榮; 盧朝勇; 林志洵; | 書刊名 | 胸腔醫學 |
卷 期 | 14:3 1999.09[民88.09] |
頁 次 | 頁127-132 |
分類號 | 416.66 |
關鍵詞 | 多發性骨髓瘤; 骨髓瘤性肋膜積液; Multiple myeloma; Myelomatous pleural effusion; |
語 文 | 英文(English) |
中文摘要 | 多發性骨髓瘤合併骨髓瘤性肋膜積液是非常罕見的疾病。我們發表一 個免疫球蛋白A-λ型多發性骨髓瘤合併骨髓瘤性肋膜積液的病例,其入院時的 症狀為呼吸困難及腰痛。胸部X光顯示右側肋膜積液,但無肋骨侵蝕。肋膜積 液之細胞學檢查顯示數量龐大的非典型性漿細胞。骨髓抽吸之細胞及組織病理學 檢查顯示明顯地非典型性漿細胞增生,吻合多發性骨髓瘤之診斷。血清電泳也顯 示免疫球蛋白A和輕鏈λ明顯地升高。因為免疫球蛋白A-λ多發性骨髓瘤之確 定診斷,我們便接著開始全身性化學治療,藥劑為oncovin, epirubicin,以及 decadron。不幸地,病人於開始化學治療後9天死於白血球過少及敗血症。 回顧過去的文獻,我們在此討論骨髓瘤性肋膜積液的病生理學,診斷,及預後。 一般而言,如果病患之肋膜積液中不正常的漿細胞數目非常多的話,細胞型態學 的檢查或許是個診斷骨髓瘤性肋膜積液的良好工具。 |
英文摘要 | Multiple myeloma(MM) complicated with myelomatous pleural effusion are rare. We present a case of immunoglobulin(Ig)A-λmultiple myeloma with myelomatous pleural effusion admitted for dyspnea and flank pain. Chest radiography showed isolated right side pleural effusion without erosion of ribs. The cytologic examination of pleural effusion revealed numerous atypical plasma cells. Cytopathologic examination of bone marrow aspiration and biopsy revealed marked proliferation of atypical plasma cells consistent with MM. Serum electrophoresis showed marked elevation of IgA and light chainλ. Systemic chemotherapy with a combination regimen of oncovin, epirubicin, and dexamethasone was subsequently initiated after documentation of IgA-λMM. Unfortunately, the patient died 9 days after chemotherapy due to leukopenia and sepsis. By a review of the literatures, the pathophysiology, diagnosis and prognosis of myelomatous pleural effusion were discussed. Morphologic examination may be a good method for the diagnosis of the myelomatous pleural effusion if there are numerous abnormal plasma cells in the pleural effusion. |
本系統中英文摘要資訊取自各篇刊載內容。