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題 名 | Bronchiolitis Obliterans and Post-Transplantation Lymphoproliferative Disorder in a Patient with Bilateral Lung Transplantation--A Case Report=肺移植後併發阻塞性細支氣管炎及淋巴增殖性疾病--一病例報告 |
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作 者 | 李乾暉; 林旻希; 賴瑞生; 盧朝勇; 許宏基; 張晃宙; 吳銘庭; 曾暉華; 王志生; | 書刊名 | 胸腔醫學 |
卷 期 | 17:4 2002.12[民91.12] |
頁 次 | 頁395-401 |
分類號 | 416.224 |
關鍵詞 | 阻塞性細支氣管炎; 肺移植; 移植後淋巴增殖性疾病; Bronchiolitis obliterans; Lung transplantation; Post-transplantation lymphoproliferative disorder; |
語 文 | 英文(English) |
中文摘要 | 對於肺功能有嚴重障礙及可預期存活時間不長的病人,肺移植提供了顯著改善生活品質及延長生命的可能性。然而,術後常出現後遺症,且限制了移植肺的功能及病患長期的存活。我們在這裡提出一個病例報告,這是一位53歲女性,臨床上出現漸進性呼吸困難,經診斷為因食用守宮木(減肥菜)造成阻塞性細支氣管炎。此病患分別接受了左肺和右肺移植。然而,在肺移植的兩年後在肺部的兩側出現了阻塞性細支氣管炎及淋巴瘤。漸進性肺功能下降以及HRCT上的特殊表現是臨床上診斷阻塞性細支管炎的線索。除此之外,在受移植者X光片上若出現新的持續性斑點或腫塊性病灶,移植後淋巴增殖性疾病應列入鑑別診斷。 |
英文摘要 | For patients with severe functional impairment of the lung and limited life expectancy, lung transplantation offers the possibility of a markedly improved quality of life and longer survival. Nonetheless, post-operation complications are frequent and result in constraints on the long term preservation of the graft function and patient survival. We present a case of a 53-year-old female who presented with progressive dyspnea and was diagnosed as bronchiolitis obliterans associated with consumption of Sauropus androgynus. The patient underwent a left and right lung transplantation, separately. However, bronchiolitis obliterans and lymphoma developed in the bilateral lungs about two years after transplantation. A progressive decline of the lung function and characteristic findings of HRCT were clues to the clinical diagnosis of identify Bo. In addition, with a new and persistent patchy or mass lesion in the chest roentgenogram in transplant recipients, post-transplantation lymphoproliferative disorder (PTLD) should be on the list of differential diagnoses. |
本系統中英文摘要資訊取自各篇刊載內容。