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題 名 | Single Lung Transplantation for Pulmonary Langerhans' Cell Histiocytosis--A Case Report=單肺移植治療肺部Langerhans'細胞組織細胞增生症--病例報告 |
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作 者 | 陳品儒; 杭良文; 林智一; 李秉純; 黃信哲; 施志勳; 許南榮; | 書刊名 | 胸腔醫學 |
卷 期 | 17:2 2002.06[民91.06] |
頁 次 | 頁143-148 |
分類號 | 415.468 |
關鍵詞 | 肺部Langerhans'細胞組織細胞增生症; 單肺移植; Pulmonary langerhans' cell histiocytosis; Single lung transplantation; |
語 文 | 英文(English) |
中文摘要 | 肺部Langerhans'細胞組織細胞增生症是一瀰漫性,和抽煙病史有關的間質性肺疾,病理上的特徵是細小支氣管有向心性發炎,形成囊泡,以及廣泛性的內因性血管病變。雖然有時會自動緩解,對一些臨床上會逐漸惡化的病例,肺臟移植可以做為治療上的選擇。在此,我們報告一28歲男性病例,因為末期的肺部Langerhans'細胞組織細胞增生症而實施右側單肺移植手術。他手術後存活,平安恢復,經6個月追縱後,肺部功能有顯著改善。 |
英文摘要 | Pulmonary langerhans' cell histicytosis (LCH) is a diffuse, smoking-related, interstitial lung disease characterized pathologically by bronchiolocentric inflammation, cyst formation, and widespread intrinsic vascular abnormalities. Despite spontaneous remissions sometimes occurring, the clinical status progressively worsens, and lung transplantation offers a therapeutic option in a few cases. The present case is a 28-year-old man who underwent right single lung transplantation (SLT) for end-stage pulmonary Langerhans' cell histiocytosis. He survived the SLT. Postoperative recovery was uneventful, and his respiratory function improved significantly after 6 months of follow-up. |
本系統中英文摘要資訊取自各篇刊載內容。