頁籤選單縮合
題 名 | Pancreatic Tumors in Children: Report of Three Cases=「小兒胰臟腫瘤」:三病例報告 |
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作 者 | 王津勝; 李宏昌; 許錦城; 張北葉; 梁德城; 陳碧芳; | 書刊名 | 臺灣兒科醫學會雜誌 |
卷 期 | 40:5 民88.09-10 |
頁 次 | 頁335-338+362 |
分類號 | 417.5462 |
關鍵詞 | 胰母細胞瘤; 硬囊腫瘤; 腹部硬塊; 體重消瘦; 慢性下痢; Pancreatoblastoma; Solid and cystic tumor; Abdominal mass; Weight loss; Chronic diarrhea; |
語 文 | 英文(English) |
中文摘要 | 小兒胰臟腫瘤,是一種罕見的疾病。馬偕醫院自1981年至1996年間,曾經成功 地診斷與治療了三個案例,年齡分別是十五天,四歲和十三歲,最後診斷,包括:兩例胰母細 胞瘤(Pancreatoblastoma)及一例硬囊腫瘤(Solid and cystic tumor)。臨床上,它們皆以腹 部硬塊,腹痛與罕有的生長遲緩,慢性下痢來表現。經過詳細的影像學(包括腹部超音波和電 腦斷層攝影)與血清學,病理學檢查:前兩例甲型胎兒蛋白有明顯上升,後一例其值正常。影 像學檢查,皆可明顯見到含有低密度的囊狀腫瘤。經過外科手術冶療,追蹤數年後,並未出 現後遺症,癒後都非常令人滿意。故我們特別提出這樣的經驗供作參考。 |
英文摘要 | From 198] to 1996, we experienced 3 cases of pancreatic tumors in children-two pancreatoblastomas (PB) and one solid and cystic tumor (SCT). The ages were I month, 4 years, and 13 years of age respectively. The two cases of pancreatoblastoma initially presented as chronic diarrhea with failure to thrive, the other case presented with abdominal mass. All of them were studied by laboratory examination, ultrasonography, computed tomography and pathology, increasing alpha-fetoprotein (AFP) levels were found in the 2 pancreatoblastoma cases, however, the level in the SCT case was normal. Abdominal sonography showed pancreatic masses with or without calcification, and the echogenicity may be solid and/or cystic. All patients underwent total excision of the tumors. We have reviewed the literature and find no pancreatoblastoma with chronic diarrhea was reported in young children, especially in neonate. Therefore, we suggest that young children presenting with an abdominal mass and/or weight loss should undergo imaging studies for the possibility of pancreatic tumors. |
本系統中英文摘要資訊取自各篇刊載內容。