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相關文獻
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題 名 | Normotensive Scleroderma Renal Crisis-A Case Report and Review of Literature=正常血壓性硬皮腎危機--病例報告與文獻回顧 |
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作 者 | 陳逸鴻; 郭弘典; 陳鴻鈞; | 書刊名 | 臺灣腎臟醫學會雜誌 |
卷 期 | 19:3 民94.09 |
頁 次 | 頁127-130+151 |
分類號 | 415.815 |
關鍵詞 | 正常血壓性硬皮腎危機; 急性腎衰竭; Normotensive scleroderma renal crisis; Acute renal failure; |
語 文 | 英文(English) |
中文摘要 | 一位七十七歲女性患有急性腎衰竭合併肺水腫,她並沒有高血壓和腎臟病史。身體物理檢查呈現手指硬化和雷諾現象,實驗室檢查呈現陽性topoisomerase抗體(scl-70)以及微血管病性溶血性貧血。腎臟切片檢查在光學顯微鏡下呈現腎絲球微血管腔狹窄和血管有onion peel(蔥皮)型態的表現,免疫螢光檢查結果是陰性的,電子顯微鏡檢查呈現嚴重腎絲球微血管基底膜皺折和足細胞突觸融合現象,並沒有電子緻密沈積物,診斷為正常血壓性硬皮腎危機。病人經採用血管張力素轉化醉抑制劑以及抗纖維化劑作治療後,其腎功能並沒有進步而且呈現透析依賴狀態。最後,她死於院內感染性肺炎併敗血性休克。 |
英文摘要 | A 77-year-old female was admitted due to acute renal failure and pulmonary edema. She had no history of hypertension or renal disease. Physical examinations showed sclerodactyly and Raynaud's phenomenon. Laboratory examination showed a positive result for topoisomerase antibody (Scl-70), and microangiopathic hemolytic anemia was also found. Renal biopsy was performed. There was a narrowing of the glomerular capillary lumen, and the vessels presented with an onion-peel picture under light microscopy. Immunofluorescent findings were negative. Electronic microscopy showed severe wrinkling change of the glomerular capillary basement membrane, and the foot processes were also effaced. There was no electron dense deposit. Normotensive scleroderma renal crisis was diagnosed. Although angiotensin converting enzyme inhibitors and antifibrotic agents were prescribed, her renal function did not improve and she became dialysis-dependent. Finally, she died of nosocomial pneumonia and subsequent septic shock. |
本系統中英文摘要資訊取自各篇刊載內容。