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題 名 | Sequential Doppler Sonographic Studies of Embolization in a Patient with Hepatic Involvement in Hereditary Hemorrhagic Telangiectasia: Correlation with Angiographic Findings=一位遺傳性出血性血管擴張症犯及肝臟之病患經肝動脈栓塞治療前後都卜勒超音波影像之變化及其與血管攝影所見之對照 |
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作 者 | 林志姮; 楊培銘; 曾旭明; 謝豐舟; | 書刊名 | 臺灣醫學會雜誌 |
卷 期 | 98:9 1999.09[民88.09] |
頁 次 | 頁633-638 |
分類號 | 415.384 |
關鍵詞 | 遺傳性出血性血管擴張症; 肝病; 肝動脈栓塞治療; 都卜勒超音波影像; 血管攝影; Osler-weber-rendu disease; Hereditary hemorrhagic telangiectasia; Doppler sonography; Hepatic angiography; Transcatheter arterial embolization; |
語 文 | 英文(English) |
英文摘要 | A 41-year-old man was admitted for symptoms of progressive congestive heart failure. His family history and the results of a physical examination were highly suggestive of Osler-Weber-Rendu disease (hereditary hemorrhagic telangiectasia, HHT). Cardiac catheterization and hepatic angiography demonstrated HHT with left-to-right shunting from the liver. The patient underwent transcatheter arterial embolization (TAE) of the right hepatic artery. We performed both Doppler sonography angiography before and after TAE. The treatment improved the clinical manifestations of congestive heart failure, including the edema of the leg and dyspnea. Doppler sonographic studies also showed an increased resistive index in the right hepatic artery and decreased flow volumes and velocities in the right and middle hepatic veins, respectively, after treatment. Corresponding changes on angiography after TAE showed decreased right hepatic arterial flow and nonopacified branches distal to the coils, disappearance of the mottled hepatogram in the right lobe, reduction of contrast agent staining, and enhanced calibers in the right and middle hepatic veins. This case illustrates that qualitative and quantitative studies with duplex and color Doppler ultrasound can be used to detect or define the extent of hepatic involvement in HHT patients before TAE, monitor hemodynamic changes of the intrahepatic vasculature after TAE, evaluate the efficacy of treatment, and possibly obviate the need for repeated angiography for diagnosis only. |
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