查詢結果分析
來源資料
頁籤選單縮合
題 名 | Atrophoderma of Pasini and Pierini--A Variant of Morphea: Report of a Case and Review of the Literature=Pasini與Pierini氏皮萎症--局限性鞏皮症之變異型:病例報告及文獻回顧 |
---|---|
作 者 | 朱家瑜; 蕭光祥; 蕭正祥; | 書刊名 | 中華皮膚科醫學雜誌 |
卷 期 | 18:4 2000.12[民89.12] |
頁 次 | 頁273-279 |
分類號 | 415.763 |
關鍵詞 | Pasini與Pierini氏皮萎症; 鞏皮症; Atrophoderma of Pasini and Pierini; Atrophoderma; |
語 文 | 英文(English) |
中文摘要 | Pasini與Pierini氏皮萎症是一種罕見但極具臨床特徵的疾病,典型皮膚病灶為境界鮮明、稍微下陷並帶有石灰色或棕色的斑,病人通常無自覺症狀,且病灶常雙側對稱出現。我們報告一例15歲女孩,最近3年來在其左側手臂及背部出現數個呈帶狀排列、稍微下陷的棕色斑。我們在其左側腰部進行皮膚切片,取下的組織包括正常皮膚與下陷部位,病理檢查發現在真皮深處局部有膠原纖維增厚及均質化的現象,因此我們診斷其為Pasini與Pierini氏皮萎症。 |
英文摘要 | Atrophoderma of Pasini and Pierini (APP) is a rare but clinically distinct skin disease characterized by sharply demarcated, slightly depressed patches with a slate-gray or brown color. The lesions are usually asymptomatic, bilateral and symmetrical. We report a 15-year-old girl who had a 3-year history of unilateral band-form, brownish, slightly depressed patches over the left arm and back. A skin biopsy from the left flank lesion including clinically normal skin and a depressed area was performed. The histopathologic study revealed thickening of the collagen fibers with homogenization in focal areas of reticular dermis at the lesion site, which is consistent with APP. |
本系統中英文摘要資訊取自各篇刊載內容。