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題 名 | Cutaneous Manifestations of Cronkhite-Canada Syndrome--A Case Report=Cronkhite-Canada徵候群的皮膚表現--病例報告 |
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作 者 | 林政賢; 陳文杰; 許明隆; 蕭嘉蓉; 許博翔; 李政昌; | 書刊名 | 中華皮膚科醫學雜誌 |
卷 期 | 19:4 2001.12[民90.12] |
頁 次 | 頁288-294 |
分類號 | 415.7 |
關鍵詞 | Cronkhite-Canada徵候群; 多發性腸胃道息肉; 指甲生長不良; 禿髮; Cronkhite-Canada syndrome; Freckle; Gastrointestinal polyposis; Onychodystrophy; |
語 文 | 英文(English) |
中文摘要 | Cronkhite-Canada徵候群(CCS)首先於1955年由Cronkhite及 Canada兩人提出,特色為多發性腸骨道息肉、皮膚色素增加、指甲生長不良及禿髮。相較於表現上述全部症狀的完全型,不完全型為缺少部分上述症狀。一位六十歲台灣籍男性近一年來有慢性腹瀉、食慾不佳及體重逐漸減輕等情形。許多類似雀斑的斑塊分布於手掌、腳掌及上肢屈側等處。二十隻手指、腳趾有輕微杵狀指及指/趾甲生長不良(特別是腳趾),並有雄性禿,而非廣泛性落髮。內視鏡及小腸系列攝影顯示出從胃到降結腸有大量的息肉;病理顯示為青年型息肉併局部腺瘤變化。進行次全大腸切除術後,指甲重新長出,但趾甲仍生長不良。於手腳掌及上肢屈側類似雀斑的斑塊顏色漸淡且數量減少。落髮狀況則維持穩定。提出此一不完全型CCS病例,並著重討論其皮膚學方面的鑑別診斷。 |
英文摘要 | Cronkhite-Canada syndrome (CCS), first described by Cronkhite and Canada in 1955, is characterized by gastrointestinal polyposis, cutaneous hyperpigmentation, onychodystrophy and alopecia. As compared with complete form of full expression, the incomplete form may lack one or some of the clinical cutaneous manifestations. A 60-year-old Taiwanese man had chronic diarrhea and poor appetite with gradual weight loss over the past one year. Numerous discrete freckle-like macules were scattered over palms and soles, as well as the flexural sides of upper extremities. All the twenty digits, toenails in particular, were slightly clubbing in shape with dystrophic nails. Male-pattern baldness rather than diffuse hair loss was observed. Endoscopy and small bowel series disclosed numerous polyps of varying sizes from the stomach to descending colon; histopathology revealed juvenile polyps with focal adenomatous change. After subtotal colectomy, fingernails have regrown but toenails remained dystrophic. Freckle-like macules over palms, soles, and flexural sides of upper extremities faded and decreased in number, while hair loss was stable. We present this case of incomplete form of CCS, and discuss the differential diagnoses in dermatological aspect. |
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