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題 名 | 鼻腔鼻竇惡性神經鞘瘤--病例報告=Sinonasal Malignant Schwannoma--Case Report |
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作 者 | 謝勇上; 周延隆; 王國榮; 彭玉文; 周建聖; | 書刊名 | 中華民國耳鼻喉科醫學雜誌 |
卷 期 | 34:5 民88.09-10 |
頁 次 | 頁408-412 |
分類號 | 416.871 |
關鍵詞 | 惡性神經鞘瘤; Malignant schwannoma; |
語 文 | 中文(Chinese) |
中文摘要 | 源於鼻腔或鼻竇的惡性神經稍瘤在文獻上少有報告。本院在1998年3月經歷一個 病例。病患為64歲女性,主訴為鼻塞6個多月,就診時在兩側鼻腔內發現有灰白色息肉狀 的腫瘤。電腦斷層顯示軟組織於兩側鼻腔及右側篩竇,經由鼻腔內視鏡手術取得的標本, 右側組織在顯微鏡下顯示惡性梭狀細胞並對S-100蛋白的染色為陽性,因而證實為惡性神 經稍瘤。病患於是再接受廣泛的內視鏡清除手術,至今年1月尚未發現有復發的現象。回 顧文獻,只有16例曾被報告過,特提出此罕見病例報告。 |
英文摘要 | Malignant schwannomas are rare neoplasms that are seldom found in the sinonasal region. The literature search reveals only 16 previously reported cases. Herein, we report a case of sinonasal malignant schwannoma which was successfully treated with endoscopic tumor excision. In 1998, a 64- year-old woman visited us with the chief complaint of nasal obstruction for more than six months. Gray-whitish polyps in both nasal cavities were found by an anterior rhinoscopy. Computed tomography (CT) scan revealed soft tissue density in both nasal cavities and the right ethmoid sinus. Bilateral chronic paranasal sinusitis with polyps was the initial impression. Endoscopic tumor excision was performed and the specimens were sent for pathologic examination. The reports revealed chronic inflammation and polyps on the left-side specimens. As for the right-side specimens, diffuse malignant spindle cells with wavy, comma shaped nuclei as well as immuno-histochemical positivity for S-100 protein and vimentin were found. Malignant schwannoma was diagnosed. Post-operative CT scan showed residual tumors in the right ethmoid sinus. The patient underwent endoscopic revision procedure to remove the tumors in the ethmoid sinus. The patient recovered with no evidence of disease 9 months after surgery. We suggest that endoscopic excision can be a viable surgical option for selective cases of malignant schwannoma in sinonasal region. |
本系統中英文摘要資訊取自各篇刊載內容。