頁籤選單縮合
題 名 | Lhermitte-Duclos Disease--First Report in Taiwan=Lhermitte-Duclos Disease--臺灣首例報告 |
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作 者 | 李建德; 何逸僊; 陳獻宗; 林子淦; 羅榮昇; | 書刊名 | 臺灣醫學會雜誌 |
卷 期 | 97:9 1998.09[民87.09] |
頁 次 | 頁649-652 |
分類號 | 417.343 |
關鍵詞 | Lhermitte-duclos disease; Dysplastic gangliocytoma; Magnetic resonance imaging; Immunohistochemistry; Cerebellar ultrastructure; |
語 文 | 英文(English) |
英文摘要 | We report a case of Lhermitte-Duclos disease (dysplastic gangliocytoma of the cerebellum), an uncommon disorder of uncertain pathogenesis characterized by disarrangement of the normal cerebellar laminar cytoarchitecture. A 40-year-old man was admitted because of vomiting and syncope of a few days' duration, and a 2-month history of intermittent headaches and unsteady gait. A computed tomographic scan of the patient's head showed obstructive hydrocephalus due to displacement of the fourth ventricle by a large, nonenhancing cerebellar mass. The magnetic resonance images of the brain also revealed a space-occupying lesion within the right cerebellum with unusual septation. After surgery, the histologic examination confirmed the diagnosis of Lhermitte-Duclos disease. This is the first report of Lhermitte-Duclos disease in Taiwan. |
本系統中英文摘要資訊取自各篇刊載內容。