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題 名 | Hemangiopericytoma of the Pleura Manifested as Massive Hemothorax: A Case Report=以大量血胸表現之肋膜血管外皮細胞瘤: 一病例報告 |
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作 者 | 阮春榮; 徐先和; 薛俊仁; 顏鴻欽; 曹唐義; 蕭海松; | 書刊名 | 中華放射線醫學雜誌 |
卷 期 | 23:5 1998.10[民87.10] |
頁 次 | 頁197-200 |
分類號 | 415.43 |
關鍵詞 | 血管外皮細胞瘤; 肋膜; 腫瘤; 出血; 電腦斷層攝影; Hemangiopericytoma; Pleura; Neoplasm; Hemorrhage; CT; |
語 文 | 英文(English) |
中文摘要 | 肋膜血管外皮細胞瘤是一種罕見且具惡傾向之血管性腫瘤,一般好發於肌肉骨骼系統、骨盆腔及後腹腔。胸腔是較不好發的部位,一般可見於肺實質、縱膈腔及胸壁。我們報告一位五十位歲男性因急性胸痛被送至急診室,胸部X光發現左側大量肋膜積水且縱膈腔被推擠至右側。電腦斷層攝影進一步顯示大量血胸及一貼近肋膜、邊緣清楚、均勻且強烈顯影之腫瘤。經手術切除及病理檢驗後證實為肋膜之血管外皮細胞瘤,腫瘤表面並有多處糜爛及出血點。回顧文獻,到目前為止並沒有出自於肋膜之血管外皮細胞瘤且合併大量血胸之病例報告。 |
英文摘要 | Hemangiopericytoma is an uncommon and potentially malignant vascular neoplasm which predominantly involves the musculoskeletal system, pelvis and retroperitoneum. Thoracic involvement is relatively rare and usually involves the lung parenchyma, mediastinum and chest wall. We report the case of a 50-year-old male who was admitted to our emergency ward due to chest pain of acute onset. Chest radiograph showed massive left plerual effusion. Contrast-enhanced computed tomography (CECT) revealed features typical of the hypervascularity seen in hemangiopericytoma including a well-defined margin. Intensely homogeneous enhancement and its pleural location were also suggestive of this diagnosis. Operative findings, microscopic and immunostaining studies led to a diagnosis of malignant hemangiopericytoma with pleural origin. To the best of our knowledge, this is the first reported case of pleural hemangiopericytoma complicated with spontaneous massive hemothorax. |
本系統中英文摘要資訊取自各篇刊載內容。