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題 名 | Carcinosarcoma of the Liver: Report of a Case=類肉瘤樣肝:一病例報告 |
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作 者 | 陳海雄; 鄭錦翔; 羅錦河; 黎國洪; 王炳惠; 潘慧本; 陳家榮; | 書刊名 | 中華民國消化系醫學雜誌 |
卷 期 | 15:2 1998.06[民87.06] |
頁 次 | 頁30-36 |
分類號 | 415.536 |
關鍵詞 | 類肉瘤樣肝癌; 免疫組織化學染色法; Hepatic carcinosarcoma; Immunohistochemical stains; |
語 文 | 英文(English) |
中文摘要 | 我們報告並討論一例經病理及特殊免疫染色法所證實的罕見之肝臟腫瘤,名為肉 瘤樣肝癌。臨床上病人表現為右上腹疼痛,電腦斷層顯示肝右葉有一巨大腫瘤且破裂至肝臟 邊緣之現象,血管攝影顯示其有豐富之血管供應,初步診斷為肝癌併有破裂現象。於是外科 醫師做了肝右葉之切除手術。病理顯示此腫瘤含有兩種成份,包括上皮細胞(肝細胞癌)及 紡綞細胞(類肉瘤),此外,腫瘤細胞有漫延過肝被膜至橫隔膜之現象;周邊之肝臟呈大結 節及小結節之肝硬化。 特殊免疫染色發現類肉瘤部份對 VIMENTIN 及 KERATIN 皆呈陽性反 應而對胎兒蛋白及癌胚胎抗原呈陰性反應。症患於開刀後三個月復發,並死於肝臟衰竭。 |
英文摘要 | We presented and discussed an unusual tumor of the liver, carcinosarcoma, which was confirmed by microscopic examination and immunohistochemical staining. Clinically the patient presented with pain in the right upper quadrant. Computerized tomography revealed a large tunor over the right lobe of the liver with rupture into the perihepatic area. Angiography further disclosed the hypervascular nature of the tumor. The diagnosis was hepatocellular carcinoma with rupture, and a right lobectomy was performed. Pathology revealed a carcinosarcoma, composed of both an epithelial component in trabecular and glandular patterns, and a sarcomatoid component with spindle cells. The tumor cells had invaded through the liver capsule to the diaphragm. The adjacent liver tissue showed macro- and micronodular cirrhosis. An immunohistochemical stain of the tumor cells of the sarcomatoid component was positive for vimentin and keratin, negative for alpha-fetoprotein and carcinoembryoinc antigen. The patient died of tumor recurrence with hepatic failure three months after the surgery. |
本系統中英文摘要資訊取自各篇刊載內容。