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題 名 | Primary Hepatic Epithelioid Hemangioendothelioma: Case Report=肝原發性類上皮血管內皮瘤:病例報告 |
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作 者 | 沈建亨; 蔡銘鴻; 陳澤卿; 劉乃仁; 沈一嫻; | 書刊名 | 長庚醫學 |
卷 期 | 22:3 1999.09[民88.09] |
頁 次 | 頁486-491 |
分類號 | 415.536 |
關鍵詞 | 肝; 類上皮血管內皮瘤; 肝膿瘍; Liver; Epithelioid hemangioendothelioma; Liver abscess; |
語 文 | 英文(English) |
中文摘要 | 肝的原發性類上皮血管內皮瘤是一種極為罕見的血管腫瘤。較常發生在成年女性, 以周邊分佈的多發性肝腫瘤來表現。因臨床表徵及影像學檢查的不具特異性,且病理組織切 片常易誤判,使得正確診斷倍加困難。雖然自然病程及預後的差異性極大,但仍優於肝血管 肉瘤。治療以腫瘤切除或肝臟移植為主。我們報告一62歲男性病人因右上腹痛而就診,最 初被診斷為肝膿瘍,經重覆肝切片檢查加上免疫組織染色,最後終於證實為肝原發性類上皮 血管內皮瘤。藉此病例報告強調肝的原發性類上皮血管內皮瘤的影像檢查及病理組織的特 徵,希望因此能讓病人早期得到正確診斷而避免接受更多不必要的檢查及處置。 |
英文摘要 | Hepatic epithelioid hemangioendothelioma (HEH) is a very rare vascular tumor of the liver. It usually affects adult women and presents as multiple hepatic nodules with mainly peripheral distribution. It poses special difficulties for clinicians in its diagnosis and treatment because of its non-specific clinical manifestations and findings on imaging, and it is easy to be misdiagnosed pathologically. Its clinical course and prognosis are variable but supposed to be intermediate between hemangioma and angiosarcoma. The primary treatments of choice are radical resection or liver transplantation. We report a 62-year-old man with right upper quadrant abdominal pain of several days' duration, who was initially misdiagnosed as having a liver abscess. Finally, HEH was diagnosed on the basis of positive immunohistochemical staining for factor VIII-related antigen in tumor cells. This case could serve to highlight the pitfalls in diagnosing this rare tumor. Increasing the index of suspicion and familiarity with the radiological and histological characteristic of this tumor would facilitate the accurate diagnosis and thus avoid unnecessary interventions. |
本系統中英文摘要資訊取自各篇刊載內容。