頁籤選單縮合
題 名 | Deogos氏症候群=Degos' Syndrome |
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作 者 | 李宗勳; 李武諺; 鄭裕文; 何宜承; 邢福柳; | 書刊名 | 中華皮膚科醫學雜誌 |
卷 期 | 16:3 1998.09[民87.09] |
頁 次 | 頁184-190 |
分類號 | 415.7 |
關鍵詞 | Deogos氏症候群; Degos' syndrome; Malignant atrophic papulosis; |
語 文 | 中文(Chinese) |
中文摘要 | 我們報告一個典型的 Degos 氏症候群病例。一位 34 歲的女性,在身上與四肢出 現許多無症狀的白色丘疹與斑塊已有六個月。 這些病灶的中央呈現如磁器般的米白色( porcelain-white center ),邊緣呈紅色而且有擴張的小血管,這樣的皮疹是 Degos 氏症 候群的特殊病徵。在接下來四個多月內病人發生數次多發性的小腸梗塞病灶,導致腸穿孔與 腹膜炎,最終造成病患死亡。 Degos 氏症候群的致病機轉至今仍不清楚。半數患者因腸胃道穿孔或中樞神經系統梗塞而死 亡。 |
英文摘要 | A typical case of Degos' syndrome is reported. The 34-year-old female patient had presented multiple asymptomatic white papuloplaques located mainly on trunk and four limbs for 6 months. These lesions show porcelain-white center with surrounding erythema and telangiectasis. The eruption is pathognomonic for malignant atrophic papulosis. Thereafter, the patient had attacks of multiple intestinal infarctions caused perforations, peritonitis, and eventually death in less than 5 months. The pathogenesis of Degos' syndrome is still unknown. Half of the patients have died from intestinal perforation or central nervous system infarcts. |
本系統中英文摘要資訊取自各篇刊載內容。