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題 名 | Primary Nonseminomatous Germ Cell Tumors of the Mediastinum=縱隔腔之原發性非精細胞型生殖細胞瘤 |
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作 者 | 陳晉興; 張逸良; 黃重傑; 李章銘; 陸希平; 李元麒; | 書刊名 | 中華民國外科醫學會雜誌 |
卷 期 | 31:5 民87.09-10 |
頁 次 | 頁301-307 |
分類號 | 415.138 |
關鍵詞 | 縱隔腔; 非精細胞型生殖細胞瘤; Nonseminomatous germ cell tumors; Mediastinum; Cisplatin-based chemotherapy; |
語 文 | 英文(English) |
中文摘要 | 臺大醫院外科從1987年至1996年共有五位男性病患因前縱隔腔之非精細胞型生殖細胞瘤接受治療。其年齡分布從9歲至39歲,睪丸檢查皆無腫瘤之侵犯。病患最常見之症狀為胸痛,腫瘤的大小則介於10.5公分至18.0公分(平均13.7公分)。四位接受腫瘤標記檢查的病患皆顯示血清之胎兒蛋白濃度有明顯上升(453.5至16469 ug/L)。五位病患皆施予超音波引導之穿刺生檢,其中只有兩位病人因此獲得確切診斷,其餘三位病人之診斷則於開胸手術後才確立。就治療方式及結果而言,第一位病患於腫瘤切除後接受化學治療,一個月後因化學治療之併發症而死亡。第二位病患則於腫瘤切除八天後因手術之併發症而死亡。 其餘三位病患於診斷確立後即接受以cisplatin為主之化學治療:其中第一位於腫瘤標記恢復正常後因胸部X光仍有殘餘腫塊而接受放射線治療,病人於手術後七個月死於腫瘤之肝臟轉移。另外兩位在接受化學治療且腫瘤標記恢復正常後,又接受手術將殘餘腫塊切除。這兩位病患目前已分別存活了9年及12個月。而言之,最近發展出來之多重治療模式,包含以cisplatin為主之化學治療,必要時再加上殘餘腫瘤之手術切除,的確提供了縱隔腔之原發性非精細胞型生殖細胞瘤病患較佳之存活機會。 |
英文摘要 | Between 1987 and 1996, five male patients ranging from 9 to 39 years old (median, 23 years), were treated for nonseminomatous germ cell tumors that appeared to arise in the anterior mediastinum without clinical involvement of the testes. The most common presenting symptom was chest pain, and the mean diameter of the tumor was 13.7 cm (range: 10.5 to 18cm). Tumor markers were measured in four patients and all had a raised alpha-fetoprotein(AFP) level (range: 453.5 ug/L to 16469 ug/L). Echo-guided needle biopsies were performed in all five patients and only two of them had definite diagnosis. The diagnosis of the other three patients could only be obtained through exploratory sternotomy. Among these five patients, one was treated with primary surgical intervention followed by chemotherapy. He died of complications of chemotherapy one month later. Another patient who received only an operation died of surgical complications eight days after the operation. The other three patients underwent cisplatin-based chemotherapy after the diagnosis of nonseminomatous germ cell tumors was made. One of them received further radiotherapy for the residual mass on chest x-ray film after normalization of the tumor markers. He died of liver metastasis 7 months after the operation. Those two patients who received surgical excision of the residual mass after completion of chemotherapy and normalization of the tumor markers were still alive at 9 years and 12 months after the operation. The modern multimodality treatment, including cisplatin-based chemotherapy coupled with adjunctive surgery if necessary, does provide a better chance of survival in our patients of primary nonseminomatous germ cell tumors of the mediastinum. |
本系統中英文摘要資訊取自各篇刊載內容。