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題 名 | POEMS Syndrome--A Case with Three-Year Follow-Up=POEMS症候群--一病例之三年追蹤 |
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作 者 | 戴仰霞; 邱顯清; | 書刊名 | 中華皮膚科醫學雜誌 |
卷 期 | 17:4 1999.12[民88.12] |
頁 次 | 頁334-338 |
分類號 | 415.78 |
關鍵詞 | POEMS症候群; POEMS syndrome; |
語 文 | 英文(English) |
中文摘要 | 我們報告一個典型的POEMS症候群病例,其表現包括漸進式之雙腳無力與麻木,甲 狀腺促進激素,雌性激素及雄性激素異常,肝脾腫大,M 蛋白質和皮膚病變。皮膚多毛,黑 色素沉積與鞏皮樣變化在疾病早期與神經病變同時發生。半年後突然長出許多血管瘤,其組 織學變化呈現許多擴張的血管分布在真皮中,但未見典型之 " 腎絲球樣血管瘤 "。 發病二 年六個月後,於右股骨頭部發現一漿細胞瘤。皮膚的黑色素沉積在漿細胞瘤切除後有明顯改 善,向管瘤在向漿交換術合併類固醇治療後完全消失。然而,神經病變卻依然如昔。 |
英文摘要 | We report a typical case of POEMS syndrome manifesting progressive weakness and numbness of bilateral lower legs, abnormal level of thyroid stimulating hormone, estrogen and testosterone, hepatosplenomegaly, M-protein and cutaneous changes. Hypertrichosis, hyperpigmentation, and sclerodermoid change of the skin appeared insidiously along with the onset of the neurological symptoms. Cutaneous angiomas were also noted in this patient, which developed abruptly about six months after the onset of the illness. Microscopically, they showed ectatic vessels in the dermis without proliferation of the endothelium. Two years and six months later, a plasmacytoma was found in the right femoral head. The cutaneous hyperpigmentation responded well to eradication of the plasmacytoma, and the angiomas totally disappeared after plasma exchange and prednisolone treatment. However, the polyneuropathy remained the same. |
本系統中英文摘要資訊取自各篇刊載內容。