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題名 | 神經腦垂體異位症併泛腦垂體機能低下--病例報告=Ectopic Neurohypophysis Associated with Panhypopituitarism |
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作者 | 廖培湧; 郭萬祐; 翁錦興; 葉步彩; 林宏達; Liao, Pei-yung; Guo, Wan-you; Won, Ging-shing; Yeh, Buh-tsai; Lin, Hong-da; |
期刊 | 中華民國內分泌暨糖尿病學會會訊 |
出版日期 | 20000400 |
卷期 | 13:3=52 2000.04[民89.04] |
頁次 | 頁18-26 |
分類號 | 415.663 |
語文 | chi |
關鍵詞 | 泛腦垂體機能低下; 神經腦垂體異位; 磁振顯影; Panhypopituitarism; Ectopic neurohypophysis; Magnetic resonance imaging; |
中文摘要 | 本文報告一位20歲泛腦垂體機能低下(congenital panhypopituitarism)的男性患者,臨床上有明顯性腺機能低下(hypogonadism)的表徵。實驗室檢查確認有腎上腺皮質機能低下,甲狀腺機能低下,性腺機能低下及輕微的高泌乳激素血症。而施行L-dopa,Clonidine或胰島素低血糖刺激試驗後,生長激素的反應都低於正常值。在腦部磁振顯影發現:腦垂體前葉發育不全併神經腦垂體異位症(ectopic neurohypophysis)及垂體柄消失。回顧文獻的記載,若影像學檢查看不到垂體柄(absence of pituitary stalk),表示其腦垂體前葉發有不全是較嚴重型,往往會同時缺乏多種前葉激素(multiple anterior pituitary hormone deficiency)。 |
英文摘要 | We report a 20-year-old man with panhypopituitarism and overt hypogonadism. The laboratory findings confirmed the diagnosis of hypocortisolism,hypothyroidism, hypogonadofaropism and mild hyperprolactinemia. Provocativetests revealed subnormal response of growth hormone to L-dopa, Clonidineand Insulin hypoglycemia stimulation. The magnetic resonance imagingstudy of brain showed : hypoplastic pituitary with ectopic neurohypophysisand absence of pituitary stalk. We reviewed the literatures and proposedthat the absence of pituitary stalk in imaging study are afflicted with amore severe form of adenohypophysis hypoplasia and have multiple anteriorpituitary hormone deficiency. |
本系統之摘要資訊系依該期刊論文摘要之資訊為主。