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題 名 | Evolution of Dilated Cardiomyopathy from Hypertrophic Obstructive Cardiomyopathy in a Child=肥厚阻塞性心肌病轉成擴張性心肌病之一兒童病例 |
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作 者 | 林于燦; 吳美環; 王主科; 呂鴻基; | 書刊名 | 臺灣醫學會雜誌 |
卷 期 | 97:6 1998.06[民87.06] |
頁 次 | 頁416-419 |
分類號 | 417.5225 |
關鍵詞 | 肥厚阻塞性心肌病; 擴張性心肌病; 兒童; Hypertrophic obstructive cardiomyopathy; Dilated cardiomyopathy; Children; |
語 文 | 英文(English) |
英文摘要 | Hypertrophic cardiomyopathy (HCM) and dilated cardiomyopathy (DCM) are two different diseases and have distinct etiologies. HCM is rare in children and rarely progresses to DCM. We report a 5-year-old Taiwanese girl with a definite diagnosis of hypertrophic obstructive cardiomyopathy. The diagnosis was based on echocardiograms, cardiac catheterization, and endomyocardial biopsy. However, the clinical features progressed to a picture of nonobstructive HCM at age 9, and the patient developed dilated poorly contractile ventricles with intractable congestive heart failure at age 10. She died from ventricular tachycardia at age 13. This report emphasizes the importance of periodic reevaluation for children with HCM. |
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