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頁籤選單縮合
題名 | Congenital Nephrotic Syndrome of the Finnish Type: Report of One Case=芬蘭型先天性腎病症候群: 一病例報告 |
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作者 | 林絹惠; 曹永魁; 蔡文雄; 陳炯暉; | 書刊名 | 中華民國小兒科醫學會雜誌 |
卷期 | 38:6 民86.11-12 |
頁次 | 頁481-483+503 |
分類號 | 417.574 |
關鍵詞 | 腎病症候群; 先天性; 芬蘭型; Congenital; Nephrotic syndrome; Finnish type; Microcystic disease; |
語文 | 英文(English) |
英文摘要 | Congenital nephrotic syndrome of Finnish type is a rare disease in Taiwan characterized by intrauterine onset of massive urinary loss of protein. We describe a typical baby of congenital nephrotic syndrome with generalized edema occurring at 3 months of age. Renal biopsy at 4 months of age showed a tubular microcystic change in histology. He had a partial response to corticosteroid. We tried persantin, indomethacin, and captopril since 10 months of age without significant improvement. The baby suffered from recurrent infections and respiratory difficulties due to having upper airway edema since 3 months of age. The baby passed away at] year and 2 months of age with severe psychomotor retardation. The first try of the combination of persantin, indomethacin, and captopril for congenital nephrotic syndrome is described. |
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