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頁籤選單縮合
題 名 | 裘馨氏肌肉失養症患者呼吸狀況的偵測=Predicting Respiratory Status in Patients with Duchenne Muscular Dystrophy |
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作 者 | 洪榮斌; 王亭貴; 盧志輝; 賴金鑫; 連倚南; | 書刊名 | 復健醫學會雜誌 |
卷 期 | 25:2 1997.12[民86.12] |
頁 次 | 頁97-104 |
分類號 | 415.96 |
關鍵詞 | 裘馨氏肌肉失養症; 夜眠呼吸監控; 肺功能檢查; 運動功能; Duchenne muscular dystrophy; Sleep breathing monitor; Pulmonary function test; Motor function; |
語 文 | 中文(Chinese) |
中文摘要 | 由裘馨氏肌肉失養症之自然病史可知,患者約於18-19歲時會因呼吸衰竭而死亡, 但患者通常在疾病末期前早已有呼吸功能異常的現象產生,而早期偵測其呼吸功能異常則有 助於早期治療,以延續其生命。 本研究採橫斷式研究, 30 名患者參與本研究,其中 19 名接受肺功能檢查四肢功能評估; 而有 10 名患者同時接受夜眠呼吸監控。 研究結果顯示接受肺功能檢查的患者中有 42% ( 8/19 )有肺功能異常,這些有肺功能異常患者均失去行走能力;在接受夜眠呼吸監控者 中有 40% ( 4/10 )有夜眠呼吸異常。肺活量小於預測值 50% 之患者,有較大機會產生夜 眠呼吸異常( 75% vs 14% ),但在統計學上並無顯著意義。 我們建議裘馨氏肌肉失養症患者,在逐漸失去行走能力時,便應至醫院接受肺功能評估,當 肺活量小於預測值之 50% 時,則應接受夜眠呼吸監控,以便早期發現及早期治療。 |
英文摘要 | The Life Expectancy of Individuals with Untreated Duchenne Muscular Dystrophy (DMD) is Around 18-19 years. The Cause of their Death is Mostly from Respiratory Complications. Early Detection of Respiratory Function will Provide the Opportunity of Early Management and Prolong Their Life Span. This Study Included 30 Patients with DMD in a Period of Three Years and Took a Crosssection design. All the data were Obtained by telephone Interview with the Patients or Their Family. Nineteen of 30 Patients Accepted Functional Evaluation in Brooke's Grading Scale and Pulmonary Function Test(PFT).Ten of These 19 Patients Received Nocturnal Breathing Monitor Including O �� Saturation and End-Tidal CO ��. The Result Showed that 8 of 19(42%) Patients who Received PFT Had Impaired Respiratory Function. All the Patients with Impaired Pulmonary Function Lost Their Ambulation Ability Simultaneously. Four of 10 Patients(40%) with Nocturnal breathing Monitor Had Nocturnal Oxygen Desaturation (NOD). The Patients whose Vital Capacity below 50% of Prediction Got a More Chance to Develop NOD, but there was no Significant Difference in Statistics. It is Suggested that DMD Patients Should Have a Routine Pulmonary Function Test Once They Progressively Lost Their Ambulation Ability. Nocturnal Breathing Monitor Should be Performed in DMD patients when their Vital Capacity was below 50% of Predicted Value for Early detection of NOD and early Management. |
本系統中英文摘要資訊取自各篇刊載內容。