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題 名 | 泛視神經脊髓炎的發展與治療=Overview of Neuromyelitis Optica Spectrum Disorder |
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作 者 | 吳芊樺; 黃俊瑋; 蔡怡倩; 朱家穎; | 書刊名 | 藥學雜誌 |
卷 期 | 33:4=133 2017.12[民106.12] |
頁 次 | 頁29-34 |
分類號 | 415.945 |
關鍵詞 | 視神經脊髓炎; 多發性硬化症; NMOSD; NMO-IgG; AQP4 antibody; MOG antibody; |
語 文 | 中文(Chinese) |
中文摘要 | 泛視神經脊髓炎 (NMOSD) 為一類嚴重的自體免疫中樞神經系統發炎性疾病。早 期因對疾病研究仍不足,易與多發性硬化症混淆,但兩者實為不同疾病,療法亦不 同。若以治療多發性硬化症 (MS) 的方式治療泛視神經脊髓炎,不但沒效果反而可能 有害。泛視神經脊髓炎發作嚴重且會復發惡化並引發永久傷害,若未有適當處置,可 能最終會呼吸衰竭死亡。已知其病理學和水通道蛋白4有關,可藉由檢驗水通道蛋白4 抗體 (AQP4-IgG) 來確認。治療則以免疫抑制療法為主,但目前尚未有國際共識,不 同國家會因取得藥物或療法的方便性,建議優先次序不同。本文簡述泛視神經脊髓炎 的發展及不同國際專家建議的治療方針供藥師參考。 |
英文摘要 | Neuromyelitis optica spectrum disorders (NMOSD) are serious autoimmune inflammatory central nervous system diseases. Due to insufficient understanding, NMOSD was easily confused with multiple sclerosis (MS) previously. Evidence showed that treated NMOSD in the same way as MS was not effective and might be harmful. It may eventually cause neurogenic respiratory failure and lead to death. Recent studies showed the pathology of NMOSD which associated with water channel aquaporin 4 (AQP4), and the detection of serum AQP4-IgG helped the diagnosis of NMOSD. Management of NMOSD with immunosuppressive therapy is the mainstay. However, there is no international consensus on the duration and regimen of therapy. The proposed medication priorities are different from international experts probably due to the accessibility of each therapy. We briefly describe the latest development of NMOSD and clinical recommendations from international experts. |
本系統中英文摘要資訊取自各篇刊載內容。