查詢結果分析
相關文獻
- Clinical Manifestations, Lymphocyte Subsets, and Complications of Patients with Common Variable Immunodeficiency in Taiwan
- HELLP Syndrome with Antepartum Pulmonary Edema--A Case Report
- Ephedrine-Induced Complete Atrioventricular Block with Ventricular Asystole during Rapid Concomitant Phenytoin Infusion: A Case Report
- Epiglottic Hematoma Secondary to Endotracheal Intubation
- 臺灣地區慢性脊髓損傷病患排尿處置之調查報告
- 小兒使用TPN引起的併發症
- 淺談糖尿病及其併發症
- 難忘的病人--民俗療法之併發症
- Clinical Experience with Ventricular Endomyocardial Biopsy in Chinese Heart Transplant Patients: A Four-Year Survey of 1,208 Consecutive Procedures
- Subcutaneous Emphysema and Pneumomediastinum Associated with Labor and Delivery
頁籤選單縮合
題 名 | Clinical Manifestations, Lymphocyte Subsets, and Complications of Patients with Common Variable Immunodeficiency in Taiwan=臺灣常見性變異性免疫不全的病人的臨床表現,淋巴細胞數目,及併發症的研究 |
---|---|
作 者 | 鄭聖翰; 藍忠亮; 謝祖怡; 陳得源; | 書刊名 | 中華民國風濕病雜誌 |
卷 期 | 21:2 2007.12[民96.12] |
頁 次 | 頁40-45 |
分類號 | 415.944 |
關鍵詞 | 常見性變異性免疫不全; 臨床表現; 併發症; 淋巴細胞數目; Common variable immunodeficiency; Clinical manifestation; Complications; Lymphocyte subsets; |
語 文 | 英文(English) |
中文摘要 | 目的:分析常見性變異性免疫不全的病人的臨床表現,淋巴細胞數目,及其併發症。 方法:在這回溯性的研究裡面,包含了12 個從1993 年到2007 年的常見性變異性免疫不全的病人。記錄了臨床的表現及併發症。用流式細胞技術來測量周邊淋巴細胞的種類。 結果:12 個病人中,8個是男性,4 個是女性。其發生常見性變異性免疫不全疾病的平均年齡是38.7 歲。免疫球蛋白G, A,M 的平均數值是 277.8, 25.6 及 34。在 8 個有測量淋巴細胞數目的病人中,其中7個的B細胞數目是不足的,其中的6個病人的 CD8 T 細胞是上升的。12 個病人的反覆性的感染,包括有肺炎,鼻竇炎,泌尿道感染,菌血症。6 個病人有慢性肺疾病,像是支氣管擴張症。三個病人有自體免疫的現象,4個病人有腫瘤疾病。 結論:我們研究的常見性變異性免疫不全的病人有比較高風險得到反覆性的感染,慢性肺疾病,腫瘤疾病,自體免疫的現象,其中自體免疫的現象包括有修格連氏症候群及抗磷脂抗症候群。 |
英文摘要 | Objective: To analyze the clinical features, lymphocyte subsets, and complications of patients with common variable immunodeficiency (CVID). Methods: In this retrospective study, twelve patients with CVID diagnosed between 1993 and 2007 were enrolled. Clinical features as well as complications were recorded. Lymphocyte subsets in the peripheralblood (PB) were analyzed using flow cytometry. Results: Eight patients (66.7%) were male and four patients (33.3%) were female and the mean age at onset was 38.7 ± 9.4 years. The mean levels of serum immunoglobulin (Ig) G, IgA and IgM were 277.8 ± 201.3 mg/dL, 25.6 ± 17.4 mg/dL, and 34.0 ± 17.2 mg/dL, respectively. Markedly decreased percentage of B cells was noted in 7 (87.5%) patients with CVID and elevated percentage of CD8+ T cell was found in 6 (75%) patients after analysis of lymphocyte subsets. Eleven of 12 had recurrent infection, including pneumonia, sinusitis, urinary tract infection and septicemia. Six of 12 had chronic lung disease, such as bronchiectasis. Three patients had autoimmune phenomenon and 4 had tumor. Conclusion: Our CVID patients had a higher risk of recurrent infection, chronic lung disease, tumor, and autoimmune phenomenon, including Sjogren’s syndrome and antiphospholipid antibody syndrome (APS). |
本系統中英文摘要資訊取自各篇刊載內容。