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題 名 | Syringoid Eccrine Carcinoma--A Case Report=汗管狀汗腺癌--病例報告 |
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作 者 | 蔡宗哲; 陳國熏; 吳介山; | 書刊名 | 中華皮膚科醫學雜誌 |
卷 期 | 25:2 2007.06[民96.06] |
頁 次 | 頁124-127 |
分類號 | 415.78 |
關鍵詞 | 汗管狀汗腺癌; 皮膚惡性腫瘤; Syringoid; Eccrine; Sweat gland neoplasm; |
語 文 | 英文(English) |
中文摘要 | 汗管狀汗腺癌是一種目前認為從汗腺延伸而來的罕見皮膚惡性腫瘤。它們會以浸潤性成長模式造成局部的侵犯。由於少見,腫瘤的起源和分化並沒有被完全確認。多樣的臨床外觀和病理組織變化使得診斷不易。我們報告一位71歲的女性在她右膝內側有個無症狀棕色的腫塊。組織病理學下看到在纖維性基質中管囊狀構造所形成的真皮內腫瘤。此腫瘤延伸整層真皮甚至接近皮下組織。這些管狀構造是由一或兩層的方狀細胞排列,其中可看到atypia與nuclear pleomorphism。Immunoperoxidase染色包跨EMA,CEA,S100,及CK7都呈現陽性反應。如此的組織病理表現與immunohistochemical 染色結果符合汗管狀汗腺癌的診斷。此腫瘤有完全的切除而全身性的檢查排除了內臟的侵犯。 |
英文摘要 | Syringoid eccrine carcinoma is a rare cutaneous malignant tumor thought to be derived from eccrine sweat apparatus. They may be locally aggressive and have an infiltrative growth pattern. Because of their rarity, the origin and differentiation of this tumor has not been confirmed completely. Variable clinical appearance and diverse histologic findings often makes diagnosis difficult. We report a 71-year-old female with an asymptomatic brownish nodule located on the medial side of right knee for years. Histopathology showed a dermal tumor consisted mainly of tubulocystic proliferation embedded in a fibrous stroma, invading the whole thickness of dermis extending close of the subcutaneous tissue. The ducts are lined by one or two layers of cuboidal cells showing variable atypia and nuclear pleomorphism. Immunoperoxidase stains with epithelial membrane antigen (EMA), carcinoembryonic antigen (CEA), CK 7 and S100 protein were all positive. Such histopathologic features and immunohistochemical profile suggest that of a syringoid eccrine carcinoma. The tumor was excised completely with free margin and systemic survey did not reveal visceral involvement. |
本系統中英文摘要資訊取自各篇刊載內容。