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題 名 | Linear IgA Disease Complicated by Erythema Multiforme=成人線狀IgA病之多形性紅斑 |
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作 者 | 梁慶瓔; | 書刊名 | 中華皮膚科醫學雜誌 |
卷 期 | 24:1 民95.03 |
頁 次 | 頁27-31 |
分類號 | 415.742 |
關鍵詞 | 成人線狀IgA病; 多形性紅斑; 水疱; Bullous disease; Dapsone; Erythema multiforme; Linear IgA dermatosis; |
語 文 | 英文(English) |
中文摘要 | 患者為男性,55歲,中國人。首發表現為臉部和身體出現許多水皰皮疹。皮膚病灶切片呈表皮下水疱。病人周圍皮膚之直接免疫螢光試驗顯示在真皮表皮交界處有線狀IgA。病人經診斷為成人線狀IgA病,給予dapsone治療得到緩解。不過病人在幾個星期後因身體出現多形性紅斑而來求診。多形性紅斑相信是因dapsone而起的副作用。成人線狀IgA病與多形性紅斑兩種病例都可能形成皮膚水疱,所以當病人在病情緩解後突然又離奇復發,必須考慮水疱病的其他診斷。本文報告一罕見病例,與討論本病臨床表現,診斷及治療方式,我們也回顧相關文獻。 |
英文摘要 | A 55-year-old Chinese man presented with acute onset of a vesicobullous rash on his face, axillae, genitalia and trunk. The skin biopsy showed a subepidermal bulla. The diagnosis was made by direct immunofluorescence of the perilesional skin which revealed characteristic linear deposition of IgA along the dermoepidermal junction. He was successfully treated with dapsone initially but subsequently developed erythema multiforme, possibly due to dapsone. Linear IgA dermatosis should be considered in patients presenting with bullous lesions, even when the distribution of the rash is atypical. Alternative diagnoses should be entertained when patients experience an unexpected relapse whilst on treatment. We highlight the important points in the clinical presentation, diagnosis and the problems encountered in the treatment of this uncommon skin disorder. |
本系統中英文摘要資訊取自各篇刊載內容。