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題 名 | Multifocal Acquired Demyelinating Sensory and Motor Neuropathy: Report of a Case and Review of the Literature=多發性後天去髓鞘感覺及運動神經病變:病例報告及文獻探討 |
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作 者 | 楊玉婉; 劉崇祥; 蔡崇豪; 李正淳; 周碩彬; | 書刊名 | Acta Neurologica Taiwanica |
卷 期 | 13:1 2004.03[民93.03] |
頁 次 | 頁24-28 |
分類號 | 415.827 |
關鍵詞 | 多發性後天去髓鞘感覺; 運動神經病變; Multifocal acquired demyelinating sensory and motor neuropathy; Asymmetric; Chronic inflammatory demyelinating polyradiculoneuropathy; Multifocal motor neuropathy; |
語 文 | 英文(English) |
英文摘要 | Multifocal acquired demyelinating sensory and motor (MADSAM) neuropathy is characterized by an asymmetric multifocal pattern of motor and sensory loss, and conduction block and other features of demyelination in nerve conduction studies. MADSAM neuropathy needs to be differentiated from chronic inflammatory demyelinating polyneuropathy (CIDP) and multifocal motor neuropathy (MMN). In classic CIDP, there are symmetric proximal and distal weakness, sensory deficit in both upper and lower extremities and reduced deep tendon reflex. In MMN, limb weakness without sensory loss is asymmetric in the distribution of individual peripheral nerves and the weakness typically begins in the distal upper extremities. We report one patient with chronic progression of asymmetric numbness and weakness in four extremities. MADSAM neuropathy was diagnosed after extensive clinical and laboratory evaluations. It is very important to distinguish between CIDP, MADSAM neuropathy, and MMN by clinical, laboratory, and histological features because of different effective therapeutic strategies. |
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