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題名 | 先天性鼻梨狀口狹窄--三例報告=Congenital Pyriform Aperture Stenosis--Report of Three Cases |
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作者 | 李振川; 李國森; 黃榮貴; 陳立盛; 翁韶嶽; 楊政謙; 張克昌; Lee, Jehn-chuan; Lee, Kuo-sheng; Huang, Jon-kway; Chen, Lih-sheng; Wong, Shau-yueh; Yang, Cheng-chien; Chang, Ko-chang; |
期刊 | 中華民國耳鼻喉科醫學會雜誌 |
出版日期 | 19980200 |
卷期 | 33:1 1998.02[民87.02] |
頁次 | 頁81-85 |
分類號 | 416.87 |
語文 | chi |
關鍵詞 | 單一上門齒; 先天性鼻梨狀口狹窄; Solitary maxillary central incisor; Congenital nasal pyiform aperture stenosis; |
中文摘要 | 先天性鼻梨狀口狹窄是造成鼻部阻塞的罕見疾病。臨床表現為鼻塞、呼吸窘迫、 周期性發紺等症狀,其症狀:與後鼻孔閉鎖極為相似。先天性鼻梨狀口狹窄可能非單一異常 ,可能與中臉成骨不全( midfacial dysostosis )合併腦下垂體內分泌軸及中樞神經系統 異常有關。單一上門齒是重要的臨床表徵,可作為早期診斷的線索。電腦斷層攝影可作正確 診斷並描述其他相關部位的異常。 治療須先考慮整體預後及狹窄程度,初期可以 McGovern 氏奶嘴維持呼吸道,若重度狹窄的話,應以唇下路徑( sublabial approach )去除過度增 生之骨性外壁。 本報告提出 3 例先天性鼻梨狀口狹窄之臨床表現及療程,並討論其病因與 治療方法。 |
英文摘要 | Congenital pyriform aperture stenosis is an uncommon cause of nasal airway obstruction in infants. This anomaly may produce manifestations of nasal airway obstruction, respiratory distress, and cyclic cyanosis similar to those seen in bilateral choanal atresia. It may represent more than an isolated congenital abnormality of the airway, and eventually may be a midfacial dysostosis with associated endocrine and central nervous system abnormalities. A solitary maxillary central incisor is the most important clue to make early diagnosis. Computed tomography confirms the diagnosis and delineates the anomaly. Managment depends firstly no overall prognosis of the patient and secondly on the severity of obstruction. The airway may be managed initially with a McGovern nipple and severely affected patients may undergo repair with a sublabial appoach to excise hypertrophic bony portion of the aperture. This article reports clinical presentation of three cases with congenital pyrifrom aperture stenosis and discusses its pathogenesis and treatment. |
本系統之摘要資訊系依該期刊論文摘要之資訊為主。