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題 名 | Solitary Infantile Myofibromatosis: Report of Two Cases=單發多樣性嬰孩型肌肉纖維瘤--二例報告 |
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作 者 | 郭芳穎; 黃純真; 邢福柳; 莊錦豪; 陳維仁; | 書刊名 | 長庚醫學 |
卷 期 | 25:6 2002.06[民91.06] |
頁 次 | 頁393-398 |
分類號 | 415.78 |
關鍵詞 | 多樣性嬰兒型肌肉纖維瘤; Infantile myofibromatosis; |
語 文 | 英文(English) |
中文摘要 | 嬰孩型肌肉纖維瘤是一個在嬰兒及兒童早期很罕見的腫瘤。這種個案典型的就是會在皮膚、軟組織、骨頭或內臟形成單一或多發性的腫瘤。本報告描述二例軟組織單發多樣性嬰孩型肌肉纖維瘤患者。第一個病例為一為7個月大的男孩,其主訴為右側大腿快速生長的腫瘤,這個大小為7×6×3.5× cm的易碎腫瘤,經由手術作完全的切除。第二個病例為一位兩歲大的男孩,其主訴為左側腹壁無壓痛性腫瘤,這個腫瘤的大小為2×2×1.6 cm,它經由手術作完全的切除。第一位病人在手術之後並沒有追蹤料,而第二位病人手術之後追蹤二十二個月後並沒有復發或惡性化轉變的情形。這個腫瘤在影像學上有不同的型態,常常酷似一個具侵襲性的腫瘤,這些因素容易造成快速及正確診斷上的困難。因此,我們建議在嬰兒幼兒時期,無論是單一或多發性的腫瘤,必須考慮嬰孩型允肉纖維瘤的可能性。 |
英文摘要 | Infantile myofibromatosis (IM) is an unusual tumor of infancy and early childhood. It typically presents as a solitary or multicentric nodular mass involving skin, soft tissue, bone, or viscera. We describe 2 cases of solitary infantile myofibromatosis (IM) of the soft tissue with typical light microscopic features. The first is a 7-month-old boy who had a rapidly growing tumor of the right thigh. The fragile tumor, measuring 7.0×6.0×3.5 cm was completely removed, but the patient was lost to follow-up after surgery. The second case, a 2-year-old boy, was referred from a local clinic due to a non-tender mass in the left abdominal wall. The tumor, measuring 2.0×2.0×1.6 cm, was completely excised. No recurrence or malignant transformation was found after 22 months of follow-up. The histopathologic, histochemical, and immunohistochemical features of the tumors were studied. Reticulin preaparation showed that the tumor cells were outside the reticulin sheath of the vascular spaces and were individually enclosed by reticulin fibers. Tests for vimentin, anti-α-smooth muscle action, and myoglobin were positive in the neoplastic spindle cells. IM has a variable appearance on radiologic images and often mimics and aggressive neoplasm. These factors can make a rapid and correct diagnosis difficult. IM must be considered in the differential diagnosis in any child who presents with either solitary or multiple tumors, particularly those occurring in the neonatal period. |
本系統中英文摘要資訊取自各篇刊載內容。