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題 名 | 丑角狀魚鱗癬--以Acitretin治療之病例報告=Harlequin Ichthyosis--Report of a Case Treated with Acitretin |
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作 者 | 許廷孚; 陳益勳; 楊國材; | 書刊名 | 中華皮膚科醫學雜誌 |
卷 期 | 18:1 2000.03[民89.03] |
頁 次 | 頁32-36 |
分類號 | 415.763 |
關鍵詞 | 丑角狀魚鱗癬; 角化; 斑色胎; Harlequin ichthyosis; Hyperkeratosis; Etretinate; |
語 文 | 中文(Chinese) |
中文摘要 | 丑角狀魚鱗癬是一種、致病原因不明的遺傳性皮膚疾病,也被認為是一種形式較嚴重、而且通常為致命性的先天性魚鱗癬。我們報告一個全身皮膚過度角化的男性嬰兒,從其臨床特徵,我們診斷為丑角狀魚鱗癬。我們在其出生第三天開始給予口服acitretin,迄今他已存活超過五個月,我們將持續追蹤他的情況。 |
英文摘要 | Harlequin ichthyosis is a rare inherited skin disorder with unknown pathogenesis and is considered to be a severe form of congenital ichthyosis and is usually fatal. We report a case of a male infant with generalized hyperkeratosis, whose clinical features were striking and characteristic for harlequin ichthyosis. Acitretin was applied from the day 3. He has survived for more than 5 months until now. We will follow-up his condition. |
本系統中英文摘要資訊取自各篇刊載內容。